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Ataluren+ Pembrolizumab

Phase 1

Colorectal Cancer | Small molecule | Oncology |PTC Therapeutics, Inc.|Last Updated: Feb 1, 2023

Target and mechanism

Molecular targetRPSA, RPS27, RPS6, RPS2, RPS3, RPS3A
Target classModulator
ModalitySmall molecule

Success Probability

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Market & Valuation

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Trial Design

CONTROLLEDDMCBiomarker
Total Trials1
Total Enrollment47

FDA Designations

No designations recorded

Clinical trial landscape

Ataluren+ Pembrolizumab · 1 trial · 2 indications

Phase 1 1
NCT04014530Pembrolizumab With Ataluren in Patients With Metastatic pMMR and dMMR Colorectal Carcinoma or Metastatic dMMR Endometrial Carcinoma: the ATAPEMBRO StudyColorectal Cancer
RECRUITING47 Analytics
PHASE1RECRUITING
Pembrolizumab With Ataluren in Patients With Metastatic pMMR and dMMR Colorectal Carcinoma or Metastatic dMMR Endometrial Carcinoma: the ATAPEMBRO Study
Colorectal CancerUnlock trial analytics

Study Endpoints

Primary Endpoints

Incidence of treatment-Emergent Adverse Event and the determination of the maximum tolerable dose of Ataluren.
Initial dose escalation for Ataluren for first 12 pt in groups of 3, which will approximately take 1 year. All adverse events will be further reported at study compeltion: expected to be after 2 years

To characterize toxicities and side effects of Ataluren when combined with pembrolizumab in patients with pMMR CRC, dMMR mCRC and dMMR EC. Recorded on Adverse Events form and ranking adverse event severity according to the NCI Common Terminology Criteria for Adverse Events v3.0

Objective response rate
30 weeks

Measured by immune-related response criteria

Secondary Endpoints

Immune-related progression free survival
21 weeks and 30 weeks
Overall survival
trough study completion: expected after 2 years.
Progression free survival
at 30 weeks
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Study Design & Arms

AllocationNON_RANDOMIZED
MaskingNONE
ModelSEQUENTIAL
PurposeTREATMENT

Treatment Arms

ArmTypeDescription
Phase I dMMR and pMMREXPERIMENTAL2-4 groups of 3 patients treatment with 200mg i.v. Pembrolizumab q3w and dose escalation of Ataluren in order to determine the Ataluren MTD. These patients can either be pMMR/dMMR CRC and dMMR EC patients.
Phase II dMMREXPERIMENTALMismatch repair deficient CRC or EC patients treated with 200mg i.v. pembrolizumab q3w and Ataluren at MTD.
Phase II pMMREXPERIMENTALMismatch repair proficient CRC patients treated with 200mg i.v. pembrolizumab q3w and Ataluren at MTD.

Interventions

NameTypeDescription
Ataluren + PembrolizumabDRUGAtaluren and Pembrolizumab combination therapy
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Eligibility Criteria

Age Range18 Years to N/A
SexALL
Healthy VolunteersNo
Study Sites1

In order to be eligible for participation in this trial, the subject must: * Have at least one lesion with measurable disease as defined by 10mm in longest diameter for a soft tissue lesions or 15mm in short axis for a lymph node by RECIST 1.1 and irRC criteria for response assessment. * Have recei...

Countries:Netherlands
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Frequently asked questions about Ataluren+ Pembrolizumab

What is Ataluren used for?

Ataluren is an investigational small molecule being studied for Duchenne muscular dystrophy (DMD), specifically nonsense mutation Duchenne muscular dystrophy, as well as aniridia, colorectal cancer, and endometrial cancer. It is being developed by PTC Therapeutics, Inc. (NASDAQ: PTCT) and is currently in Phase 2 clinical development.

How does Ataluren work?

Ataluren is designed to enable the read-through of premature stop codons in messenger RNA, allowing the production of full-length, functional proteins in patients with nonsense mutations. This mechanism is relevant for genetic disorders like Duchenne muscular dystrophy caused by nonsense mutations, though the specific molecular target has not been disclosed.

Who makes Ataluren?

Ataluren is being developed by PTC Therapeutics, Inc., a biopharmaceutical company traded on NASDAQ under the ticker symbol PTCT. The company is conducting clinical trials of Ataluren across multiple indications, including Duchenne muscular dystrophy and certain cancers.

What phase is Ataluren in?

Ataluren is in Phase 2 clinical development. It has completed Phase 3 trials for nonsense mutation Duchenne muscular dystrophy, and a Phase 1 trial combining Ataluren with pembrolizumab is currently recruiting patients with metastatic colorectal or endometrial cancer. Ataluren remains investigational and is not FDA approved.

What clinical trials is Ataluren in?

Ataluren has been studied in several clinical trials, including NCT01826487, a completed Phase 3 study in nonsense mutation Duchenne muscular dystrophy with 230 participants, and NCT03179631, a completed Phase 3 long-term outcomes study with 360 participants. An active Phase 1 trial, NCT04014530, is evaluating Ataluren with pembrolizumab in colorectal and endometrial cancers.

Is Ataluren the same as Ataluren plus Pembrolizumab?

Ataluren plus Pembrolizumab is a combination regimen being studied in clinical trials, not a separate drug name. The combination is being evaluated in the ATAPEMBRO study (NCT04014530) for metastatic colorectal and endometrial cancers, where Ataluren is administered alongside the immunotherapy pembrolizumab.