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AMX0114

Phase 1

ALS | Small molecule | Neurology |Amylyx Pharmaceuticals, Inc.|Last Updated: Apr 14, 2026

Target and mechanism

Molecular targetcalpain-2
Target classProtein
ModalitySmall molecule

Success Probability

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Market & Valuation

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Trial Design

RandomizedDouble-BlindPLACEBO_CONTROLLEDDMC
Total Trials1
Total Enrollment48

FDA Designations

No designations recorded

Clinical trial landscape

AMX0114 · 1 trial · 1 indication

Phase 1 1
NCT06665165AMX0114 in Adult Participants With Amyotrophic Lateral SclerosisALS
RECRUITING48 Analytics
PHASE1RECRUITING
AMX0114 in Adult Participants With Amyotrophic Lateral Sclerosis
ALSUnlock trial analytics

Study Endpoints

Primary Endpoints

Evaluate the safety and tolerability of AMX0114 in adult participants living with ALS
Day 1 - Day 145 (End of Study)

Incidence of adverse events (AEs), serious adverse events (SAEs) and dose limiting toxicities (DLTs). Incidence of abnormalities in clinical laboratory assessments, vital signs, physical and neurological examinations, and electrocardiograms (ECGs).

Secondary Endpoints

Evaluate the PK of AMX0114
Day 1 - Day 145 (End of Study)
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Study Design & Arms

AllocationRANDOMIZED
MaskingQUADRUPLE
ModelSEQUENTIAL
PurposeTREATMENT

Treatment Arms

ArmTypeDescription
Active Treatment: AMX0114EXPERIMENTALAMX0114 will be administered once every 4 weeks by intrathecal bolus injection for a total of up to 4 doses. Treatment will be administered on Day 1, followed by repeat dosing every 4 weeks at approximately Day 29, Day 57 and Day 85.
PlaceboPLACEBO_COMPARATORPlacebo drug will be administered once every 4 weeks by intrathecal bolus injection for a total of up to 4 doses. Treatment will be administered on Day 1, followed by repeat dosing every 4 weeks at approximately Day 29, Day 57 and Day 85.

Interventions

NameTypeDescription
AMX0114DRUGAntisense oligonucleotides (ASOs) are a type of medicine that treats diseases by intercepting the mRNA messages sent within the cell, resulting in fewer specific proteins being made. AMX0114 is an ASO that targets the mRNA messenger that instructs the body to create a protein called calpain-2. Calpain-2 has been linked to the degeneration and death of neurons in many neurological diseases, including people living with sporadic ALS. AMX0114 is designed to reduce the levels of calpain-2, with the goal of slowing down the process that leads to neuron injury and death.
PlaceboOTHERPlacebo
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Eligibility Criteria

Age Range18 Years to N/A
SexALL
Healthy VolunteersNo
Study Sites14

Inclusion Criteria: 1. Ability to understand the purpose and risks of this study, willingness to comply with the study and to provide informed consent in accordance with local laws and regulations. 2. Male or female, at least 18 years of age. 3. Diagnosis of clinically definite or clinically probab...

Countries:United StatesCanada
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Recent Changes (Last 90 Days)

LOWMay 26, 2026NCT06665165primaryCompletionDate: changed
LOWMay 24, 2026NCT06665165studyFirstPostDate: changed

Frequently asked questions about AMX0114

What is AMX0114 used for in ALS?

AMX0114 is an investigational small molecule being developed for the treatment of amyotrophic lateral sclerosis (ALS). It is currently in Phase 1 clinical development and has not been approved by regulatory authorities. The drug is being studied in adult participants with ALS in a clinical trial.

What does AMX0114 target?

AMX0114 targets calpain-2, a protein involved in cellular processes. By modulating this target, the drug aims to address pathways relevant to ALS. The specific mechanism of action is under investigation in clinical trials.

Who makes AMX0114?

AMX0114 is being developed by Amylyx Pharmaceuticals, Inc., a biopharmaceutical company. The company is conducting clinical trials to evaluate the safety and efficacy of AMX0114 in patients with ALS.

What phase is AMX0114 in?

AMX0114 is in Phase 1 clinical development. It is currently being evaluated in a randomized, double-blind, placebo-controlled trial in adult participants with ALS. The drug is investigational and has not yet received regulatory approval.

What clinical trials is AMX0114 in?

AMX0114 is being studied in a Phase 1 clinical trial with the identifier NCT06665165. This trial is recruiting participants with ALS in the United States and Canada, with an enrollment target of 48 participants. The study is randomized, double-blind, and placebo-controlled.