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AMX0114

Phase 1

ALS | Small molecule | Neurology |Amylyx Pharmaceuticals, Inc.|Last Updated: Apr 14, 2026

Target and mechanism

Molecular targetcalpain-2
Target classProtein
ModalitySmall molecule

Success Probability

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Market & Valuation

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Trial Design

RandomizedDouble-BlindPLACEBO_CONTROLLEDDMC
Total Trials1
Total Enrollment48

FDA Designations

No designations recorded

Clinical trial landscape

AMX0114 · 1 trial · 1 indication

Phase 1 1
NCT06665165AMX0114 in Adult Participants With Amyotrophic Lateral SclerosisALS
RECRUITING48 Analytics
PHASE1RECRUITING
AMX0114 in Adult Participants With Amyotrophic Lateral Sclerosis
ALSUnlock trial analytics

Study Endpoints

Primary Endpoints

Evaluate the safety and tolerability of AMX0114 in adult participants living with ALS
Day 1 - Day 145 (End of Study)

Incidence of adverse events (AEs), serious adverse events (SAEs) and dose limiting toxicities (DLTs). Incidence of abnormalities in clinical laboratory assessments, vital signs, physical and neurological examinations, and electrocardiograms (ECGs).

Secondary Endpoints

Evaluate the PK of AMX0114
Day 1 - Day 145 (End of Study)
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Study Design & Arms

AllocationRANDOMIZED
MaskingQUADRUPLE
ModelSEQUENTIAL
PurposeTREATMENT

Treatment Arms

ArmTypeDescription
Active Treatment: AMX0114EXPERIMENTALAMX0114 will be administered once every 4 weeks by intrathecal bolus injection for a total of up to 4 doses. Treatment will be administered on Day 1, followed by repeat dosing every 4 weeks at approximately Day 29, Day 57 and Day 85.
PlaceboPLACEBO_COMPARATORPlacebo drug will be administered once every 4 weeks by intrathecal bolus injection for a total of up to 4 doses. Treatment will be administered on Day 1, followed by repeat dosing every 4 weeks at approximately Day 29, Day 57 and Day 85.

Interventions

NameTypeDescription
AMX0114DRUGAntisense oligonucleotides (ASOs) are a type of medicine that treats diseases by intercepting the mRNA messages sent within the cell, resulting in fewer specific proteins being made. AMX0114 is an ASO that targets the mRNA messenger that instructs the body to create a protein called calpain-2. Calpain-2 has been linked to the degeneration and death of neurons in many neurological diseases, including people living with sporadic ALS. AMX0114 is designed to reduce the levels of calpain-2, with the goal of slowing down the process that leads to neuron injury and death.
PlaceboOTHERPlacebo
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Eligibility Criteria

Age Range18 Years to N/A
SexALL
Healthy VolunteersNo
Study Sites14

Inclusion Criteria: 1. Ability to understand the purpose and risks of this study, willingness to comply with the study and to provide informed consent in accordance with local laws and regulations. 2. Male or female, at least 18 years of age. 3. Diagnosis of clinically definite or clinically probab...

Countries:United StatesCanada
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Frequently asked questions about AMX0114

What is AMX0114 used for in ALS?

AMX0114 is an investigational small molecule being developed for the treatment of amyotrophic lateral sclerosis (ALS). It is currently in Phase 1 clinical development and has not been approved by the FDA. The drug is being studied in adult participants with ALS in a randomized, double-blind, placebo-controlled trial.

What does AMX0114 target?

AMX0114 targets calpain-2, a protein that belongs to the calpain family of proteases. By inhibiting calpain-2, the drug aims to modulate pathways involved in ALS pathology. This mechanism is being evaluated in early-stage clinical trials to assess its safety and tolerability in patients.

Who makes AMX0114?

AMX0114 is being developed by Amylyx Pharmaceuticals, Inc., a biopharmaceutical company traded on the NASDAQ under the ticker symbol AMLX. The company is conducting a Phase 1 clinical trial of AMX0114 in the United States and Canada for the treatment of ALS.

What phase is AMX0114 in?

AMX0114 is currently in Phase 1 clinical development. It is an investigational drug and has not received FDA approval. The ongoing Phase 1 trial is recruiting participants with ALS and is designed to evaluate the drug's safety, tolerability, and pharmacokinetics in a randomized, placebo-controlled setting.

What clinical trials is AMX0114 in?

AMX0114 is being studied in a single Phase 1 clinical trial with the identifier NCT06665165, titled 'AMX0114 in Adult Participants With Amyotrophic Lateral Sclerosis.' The trial is recruiting 48 participants in the United States and Canada, and it is a randomized, double-blind, placebo-controlled study.