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ARGX-119

Phase 1

Congenital Myasthenic Syndrome | Monoclonal antibody | Rare Disease |argenx SE|Last Updated: Apr 23, 2026

Success Probability
Approval Probability 71%
TA Base Rate26%
Adjusted LOA41%
ML RiskLOW_RISK
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Market & Valuation
rNPV $3.2B
Market Size $9.4B
Revenue Basis $1.6B
Competitors 6
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Trial Design
RandomizedDouble-BlindPLACEBO_CONTROLLEDBiomarker
Total Trials1
Total Enrollment16
FDA Designations
No designations recorded
Clinical Trials (1)
NCT IDTitlePhaseStatusEnrollmentVelocityDesignStartCompletionLast UpdatedSitesCountries
NCT06436742A Phase 1b Study to Investigate Safety and Tolerability of ARGX-119 in Adult Participants With DOK7-Congenital Myasthenic Syndromes (CMS)PHASE1 RECRUITING 16Sep 24, 2024Jan 24, 2028Apr 23, 20269 United States, Canada +4
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Study Endpoints
Primary Endpoints
Assessment of adverse events (AEs)
Up to week 42
Change from active-treatment baseline over time for 6MWT distance
Up to 72 weeks

The 6-minute walk test (6MWT) measures the distance a participant walks in 6 minutes. Before and after the 6MWT assessment, the participant's blood pressure, heart rate, and SPO2 will be recorded, and the participant's perception of fatigue and dyspnea will be measured.

Secondary Endpoints
Maximum observed serum concentration (Cmax) of ARGX-119
Up to 42 weeks + 72 weeks
Incidence of ADA against ARGX-119
Up to 42 weeks + 72 weeks
Change from baseline over time for key components of the QMG scale
Up to 42 weeks + 72 weeks
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Study Design & Arms
AllocationRANDOMIZED
MaskingQUADRUPLE
ModelPARALLEL
PurposeTREATMENT
Treatment Arms
ArmTypeDescription
Double-blinded treatment period - ARGX-119 IVEXPERIMENTALParticipants receive ARGX-119 during the double-blinded treatment period
Double-blinded treatment period - Placebo IVPLACEBO_COMPARATORParticipants receive placebo during the double-blinded treatment period
Active-treatment period - ARGX-119 IVEXPERIMENTALParticipants receive ARGX-119 during the active-treatment period
Interventions
NameTypeDescription
ARGX-119BIOLOGICALIntravenous infusion of ARGX-119
PlaceboOTHERIntravenous infusion of placebo
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Eligibility Criteria
Age Range18 Years — N/A
SexALL
Healthy VolunteersNo
Study Sites9

Inclusion Criteria: * At least 18 years of age. * Has genetically confirmed congenital myasthenic syndromes due to mutation of downstream of kinase 7 (DOK7-CMS). * Participants taking oral beta agonists (eg, albuterol, salbutamol, ephedrine) must have been receiving the medication for more than 3 m...

Countries:United StatesCanadaFranceItalySpainUnited Kingdom
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Recent Changes (Last 90 Days)
LOWMay 26, 2026NCT06436742primaryCompletionDate: changed
LOWMay 24, 2026NCT06436742studyFirstPostDate: changed