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AMT-162

Phase 1

Amyotrophic Lateral Sclerosis | Small molecule | Neurology |uniQure N.V.|Last Updated: Oct 22, 2025

Success Probability
Approval Probability 71%
TA Base Rate26%
Adjusted LOA41%
ML RiskLOW_RISK
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Market & Valuation
rNPV $3.2B
Market Size $9.4B
Revenue Basis $1.6B
Competitors 6
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Trial Design
CONTROLLEDDMC
Total Trials1
Total Enrollment20
FDA Designations
No designations recorded
Clinical Trials (1)
NCT IDTitlePhaseStatusEnrollmentVelocityDesignStartCompletionLast UpdatedSitesCountries
NCT06100276Safety, Tolerability, and Exploratory Efficacy Study of Intrathecally Administered Gene Therapy AMT-162 in Adult Participants With SOD1 Amyotrophic Lateral Sclerosis (SOD1-ALS)PHASE1 ACTIVE NOT_RECRUITING 20Aug 1, 2024Jun 30, 2031Oct 22, 202512 United States, Sweden
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Study Endpoints
Primary Endpoints
To evaluate the safety and tolerability of ascending doses of intrathecally administered AMT-162 in Participants with SOD1-ALS
up to 5 years

Occurrence of TEAEs upon administration of ascending doses of AMT-162

Secondary Endpoints
Characterization of Immune Response to AMT-162 and Shedding of intrathecally administered AMT-162.
up to 5 years
Characterization of the Effect of intrathecally administered AMT-162
up to 5 years
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Study Design & Arms
AllocationNON_RANDOMIZED
MaskingNONE
ModelSEQUENTIAL
PurposeTREATMENT
Treatment Arms
ArmTypeDescription
3 single Ascending Dose LevelsEXPERIMENTALExperimental: 3 single Ascending Dose Levels The study will be open-label with an initial plan to explore 3 dose levels of AMT-162 in approximately 6 to 12 Participants in total. Each Participant will receive a single dose of AMT-162 delivered via an intrathecal (IT) infusion and will be followed for up to 5 years after AMT-162 administration.
EXPANSION COHORTEXPERIMENTALExpansion cohort: To further test selected dose from the SAD part in approximately 6 to 8 participants The study will be open-label. Each Participant will receive a single dose of AMT-162 delivered via an intrathecal (IT) infusion and will be followed for up to 5 years after AMT-162 administration.
Interventions
NameTypeDescription
AMT-162DRUGAMT-162, the investigational product (IP), is a nonreplicating, rep/cap-deleted, self-complementary Recombinant adeno-associated virus (rAAV) vector based on adeno-associated virus (AAV) serotype rh10 and contains complementary deoxyribonucleic acid (cDNA) encoding an artificial miRNA targeting the SOD1 gene.
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Eligibility Criteria
Age Range18 Years — N/A
SexALL
Healthy VolunteersNo
Study Sites12

Inclusion Criteria: * Confirmed clinical and genetic diagnosis of SOD1-mediated ALS (SOD1-ALS) experiencing signs and/or symptoms of lower motor neuron dysfunction (weakness, atrophy, cramps, fasciculations), with or without upper motor neuron symptoms (weakness, bring reflexes, spasticity). * ALSF...

Countries:United StatesSweden
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Recent Changes (Last 90 Days)
LOWMay 26, 2026NCT06100276primaryCompletionDate: changed
LOWMay 24, 2026NCT06100276studyFirstPostDate: changed