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AMT-162

Phase 1

Amyotrophic Lateral Sclerosis | Small molecule | Neurology |uniQure N.V.|Last Updated: Oct 22, 2025

Target and mechanism

Molecular targetSOD1
Target classGene
ModalitySmall molecule

Success Probability

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Market & Valuation

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Trial Design

CONTROLLEDDMC
Total Trials1
Total Enrollment20

FDA Designations

No designations recorded

Clinical trial landscape

AMT-162 · 1 trial · 1 indication

Phase 1 1
NCT06100276Safety, Tolerability, and Exploratory Efficacy Study of Intrathecally Administered Gene Therapy AMT-162 in Adult Participants With SOD1 Amyotrophic Lateral Sclerosis (SOD1-ALS)Amyotrophic Lateral Sclerosis
ACTIVE NOT_RECRUITING20 Analytics
PHASE1ACTIVE NOT_RECRUITING
Safety, Tolerability, and Exploratory Efficacy Study of Intrathecally Administered Gene Therapy AMT-162 in Adult Participants With SOD1 Amyotrophic Lateral Sclerosis (SOD1-ALS)
Amyotrophic Lateral SclerosisUnlock trial analytics

Study Endpoints

Primary Endpoints

To evaluate the safety and tolerability of ascending doses of intrathecally administered AMT-162 in Participants with SOD1-ALS
up to 5 years

Occurrence of TEAEs upon administration of ascending doses of AMT-162

Secondary Endpoints

Characterization of Immune Response to AMT-162 and Shedding of intrathecally administered AMT-162.
up to 5 years
Characterization of the Effect of intrathecally administered AMT-162
up to 5 years
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Study Design & Arms

AllocationNON_RANDOMIZED
MaskingNONE
ModelSEQUENTIAL
PurposeTREATMENT

Treatment Arms

ArmTypeDescription
3 single Ascending Dose LevelsEXPERIMENTALExperimental: 3 single Ascending Dose Levels The study will be open-label with an initial plan to explore 3 dose levels of AMT-162 in approximately 6 to 12 Participants in total. Each Participant will receive a single dose of AMT-162 delivered via an intrathecal (IT) infusion and will be followed for up to 5 years after AMT-162 administration.
EXPANSION COHORTEXPERIMENTALExpansion cohort: To further test selected dose from the SAD part in approximately 6 to 8 participants The study will be open-label. Each Participant will receive a single dose of AMT-162 delivered via an intrathecal (IT) infusion and will be followed for up to 5 years after AMT-162 administration.

Interventions

NameTypeDescription
AMT-162DRUGAMT-162, the investigational product (IP), is a nonreplicating, rep/cap-deleted, self-complementary Recombinant adeno-associated virus (rAAV) vector based on adeno-associated virus (AAV) serotype rh10 and contains complementary deoxyribonucleic acid (cDNA) encoding an artificial miRNA targeting the SOD1 gene.
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Eligibility Criteria

Age Range18 Years to N/A
SexALL
Healthy VolunteersNo
Study Sites12

Inclusion Criteria: * Confirmed clinical and genetic diagnosis of SOD1-mediated ALS (SOD1-ALS) experiencing signs and/or symptoms of lower motor neuron dysfunction (weakness, atrophy, cramps, fasciculations), with or without upper motor neuron symptoms (weakness, bring reflexes, spasticity). * ALSF...

Countries:United StatesSweden
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Recent Changes (Last 90 Days)

LOWMay 26, 2026NCT06100276primaryCompletionDate: changed
LOWMay 24, 2026NCT06100276studyFirstPostDate: changed

Frequently asked questions about AMT-162

What is AMT-162 used for?

AMT-162 is an investigational gene therapy being developed for the treatment of Amyotrophic Lateral Sclerosis (ALS), specifically in adult participants with SOD1-ALS. It is administered intrathecally. The drug is currently in Phase 1 clinical development and is not yet approved by regulatory authorities.

What does AMT-162 target?

AMT-162 targets the SOD1 gene, which is implicated in a form of Amyotrophic Lateral Sclerosis known as SOD1-ALS. By targeting this gene, the therapy aims to address the underlying genetic cause of the disease. The drug is designed for intrathecal administration to deliver the gene therapy directly to the central nervous system.

Who makes AMT-162?

AMT-162 is being developed by uniQure N.V., a biopharmaceutical company. The company's stock is traded under the ticker symbol QURE. uniQure is conducting clinical trials to evaluate the safety, tolerability, and exploratory efficacy of AMT-162 in patients with SOD1-ALS.

What phase is AMT-162 in?

AMT-162 is currently in Phase 1 clinical development. It is an investigational drug, meaning it has not been approved by the FDA or other regulatory agencies. The ongoing Phase 1 trial is active but not recruiting participants, and it is designed to assess the safety, tolerability, and exploratory efficacy of the therapy.

What clinical trials is AMT-162 in?

AMT-162 is being studied in a Phase 1 clinical trial with the identifier NCT06100276. This trial is titled 'Safety, Tolerability, and Exploratory Efficacy Study of Intrathecally Administered Gene Therapy AMT-162 in Adult Participants With SOD1 Amyotrophic Lateral Sclerosis (SOD1-ALS)'. The trial is active but not recruiting, with an enrollment of 20 participants in the United States and Sweden.

Is AMT-162 the same as SOD1-ALS gene therapy?

AMT-162 is a gene therapy specifically designed for SOD1-ALS, a form of Amyotrophic Lateral Sclerosis caused by mutations in the SOD1 gene. While it is not known by other names, it is often referred to as an SOD1-ALS gene therapy in clinical trial descriptions. The therapy is administered intrathecally to target the central nervous system.