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AMT-162

Phase 1

Amyotrophic Lateral Sclerosis | Small molecule | Neurology |uniQure N.V.|Last Updated: Oct 22, 2025

Target and mechanism

Molecular targetSOD1
Target classGene
ModalitySmall molecule

Success Probability

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Market & Valuation

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Trial Design

CONTROLLEDDMC
Total Trials1
Total Enrollment20

FDA Designations

No designations recorded

Clinical trial landscape

AMT-162 · 1 trial · 1 indication

Phase 1 1
NCT06100276Safety, Tolerability, and Exploratory Efficacy Study of Intrathecally Administered Gene Therapy AMT-162 in Adult Participants With SOD1 Amyotrophic Lateral Sclerosis (SOD1-ALS)Amyotrophic Lateral Sclerosis
ACTIVE NOT_RECRUITING20 Analytics
PHASE1ACTIVE NOT_RECRUITING
Safety, Tolerability, and Exploratory Efficacy Study of Intrathecally Administered Gene Therapy AMT-162 in Adult Participants With SOD1 Amyotrophic Lateral Sclerosis (SOD1-ALS)
Amyotrophic Lateral SclerosisUnlock trial analytics

Study Endpoints

Primary Endpoints

To evaluate the safety and tolerability of ascending doses of intrathecally administered AMT-162 in Participants with SOD1-ALS
up to 5 years

Occurrence of TEAEs upon administration of ascending doses of AMT-162

Secondary Endpoints

Characterization of Immune Response to AMT-162 and Shedding of intrathecally administered AMT-162.
up to 5 years
Characterization of the Effect of intrathecally administered AMT-162
up to 5 years
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Study Design & Arms

AllocationNON_RANDOMIZED
MaskingNONE
ModelSEQUENTIAL
PurposeTREATMENT

Treatment Arms

ArmTypeDescription
3 single Ascending Dose LevelsEXPERIMENTALExperimental: 3 single Ascending Dose Levels The study will be open-label with an initial plan to explore 3 dose levels of AMT-162 in approximately 6 to 12 Participants in total. Each Participant will receive a single dose of AMT-162 delivered via an intrathecal (IT) infusion and will be followed for up to 5 years after AMT-162 administration.
EXPANSION COHORTEXPERIMENTALExpansion cohort: To further test selected dose from the SAD part in approximately 6 to 8 participants The study will be open-label. Each Participant will receive a single dose of AMT-162 delivered via an intrathecal (IT) infusion and will be followed for up to 5 years after AMT-162 administration.

Interventions

NameTypeDescription
AMT-162DRUGAMT-162, the investigational product (IP), is a nonreplicating, rep/cap-deleted, self-complementary Recombinant adeno-associated virus (rAAV) vector based on adeno-associated virus (AAV) serotype rh10 and contains complementary deoxyribonucleic acid (cDNA) encoding an artificial miRNA targeting the SOD1 gene.
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Eligibility Criteria

Age Range18 Years to N/A
SexALL
Healthy VolunteersNo
Study Sites12

Inclusion Criteria: * Confirmed clinical and genetic diagnosis of SOD1-mediated ALS (SOD1-ALS) experiencing signs and/or symptoms of lower motor neuron dysfunction (weakness, atrophy, cramps, fasciculations), with or without upper motor neuron symptoms (weakness, bring reflexes, spasticity). * ALSF...

Countries:United StatesSweden
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Frequently asked questions about AMT-162

What is AMT-162 used for?

AMT-162 is an investigational gene therapy being developed for the treatment of Amyotrophic Lateral Sclerosis (ALS) in adult participants with SOD1-ALS. It is administered intrathecally and is currently in Phase 1 clinical development.

What does AMT-162 target?

AMT-162 targets the SOD1 gene, which is associated with a form of Amyotrophic Lateral Sclerosis known as SOD1-ALS. By targeting this gene, the therapy aims to address the underlying genetic cause of the disease.

Who makes AMT-162?

AMT-162 is being developed by uniQure N.V., a biopharmaceutical company listed on the stock exchange under the ticker symbol QURE. The company is conducting clinical trials to evaluate the safety and efficacy of this investigational therapy.

What phase is AMT-162 in?

AMT-162 is currently in Phase 1 clinical development. It is an investigational drug and has not yet been approved by regulatory authorities. The ongoing Phase 1 trial is designed to assess its safety, tolerability, and exploratory efficacy.

What clinical trials is AMT-162 in?

AMT-162 is being studied in a Phase 1 clinical trial with the identifier NCT06100276. This trial is titled 'Safety, Tolerability, and Exploratory Efficacy Study of Intrathecally Administered Gene Therapy AMT-162 in Adult Participants With SOD1 Amyotrophic Lateral Sclerosis (SOD1-ALS)' and is currently active but not recruiting.

Is AMT-162 the same as a gene therapy for ALS?

AMT-162 is a gene therapy specifically designed for SOD1-ALS, a genetic form of Amyotrophic Lateral Sclerosis. It is administered intrathecally and targets the SOD1 gene. The ongoing Phase 1 trial is enrolling participants in the United States and Sweden.