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AVXS-101

Phase 1

Spinal Muscular Atrophy 1 | Monoclonal antibody | Neurology |Novartis AG|Last Updated: Sep 15, 2022

Success Probability

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Market & Valuation

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Trial Design

CONTROLLEDDMC
Total Trials1
Total Enrollment15

FDA Designations

No designations recorded

Clinical trial landscape

AVXS-101 · 1 trial · 1 indication

Phase 1 1
NCT02122952Gene Transfer Clinical Trial for Spinal Muscular Atrophy Type 1Spinal Muscular Atrophy 1
COMPLETED15 Analytics
PHASE1COMPLETED
Gene Transfer Clinical Trial for Spinal Muscular Atrophy Type 1
Spinal Muscular Atrophy 1Unlock trial analytics

Study Endpoints

Primary Endpoints

Number of Participants That Experienced One Grade III or Higher Unanticipated, Treatment-related Toxicity That Presents With Clinical Symptoms and Requires Medical Treatment
2 years

Secondary Endpoints

Number of Participants Who Experienced Permanent Ventilation or Death
Up to 13.6 months of age
Percent Change From Baseline in Mean Children's Hospital of Philadelphia Infant Test of Neuromuscular Disorders (CHOP-INTEND) Score
Baseline to 24 months post-dose
Number of Participants With Assessed Improvement in Motor Function
24 months post-dose
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Study Design & Arms

AllocationNON_RANDOMIZED
MaskingNONE
ModelSINGLE_GROUP
PurposeTREATMENT

Treatment Arms

ArmTypeDescription
Cohort 1EXPERIMENTAL6.7 X 10\^13 vg/kg of AVXS-101 delivered one-time through a venous catheter inserted into a peripheral vein (n=3)
Cohort 2EXPERIMENTAL2.0 X 10\^14 vg/kg of AVXS-101 delivered one-time through a venous catheter inserted into a peripheral vein (n=12)

Interventions

NameTypeDescription
AVXS-101BIOLOGICALSelf-complementary AAV9 carrying the SMN gene under the control of a hybrid CMV enhancer/chicken-β-actin promoter
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Eligibility Criteria

Age RangeN/A to 6 Months
SexALL
Healthy VolunteersNo
Study Sites1

Inclusion Criteria: * Six or nine months of age and younger (depending on cohort) on day of vector infusion with Type 1 SMA as defined by the following features: * Diagnosis of SMA based on gene mutation analysis with bi-allelic SMN1 mutations (deletion or point mutations) and 2 copies of SMN2. ...

Countries:United States
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Competitive Landscape -Spinal Muscular Atrophy 27 trials (matched to "Spinal Muscular Atrophy 1")

Frequently asked questions about AVXS-101

What is AVXS-101 used for?

AVXS-101 is an investigational gene therapy being developed for the treatment of Spinal Muscular Atrophy 1, a severe genetic disorder affecting motor neurons. It is currently in clinical development and has not been approved by regulatory authorities.

Who makes AVXS-101?

AVXS-101 is developed by Novartis AG, a multinational pharmaceutical company listed on the New York Stock Exchange under the ticker symbol NVS. The drug is being studied for Spinal Muscular Atrophy 1.

What phase is AVXS-101 in?

AVXS-101 is in Phase 1 clinical development. It is an investigational drug, meaning it has not yet been approved by regulatory agencies. The Phase 1 trial for Spinal Muscular Atrophy 1 has been completed.

What clinical trials is AVXS-101 in?

AVXS-101 has one completed clinical trial, identified as NCT02122952, titled 'Gene Transfer Clinical Trial for Spinal Muscular Atrophy Type 1'. This Phase 1 study enrolled 15 participants in the United States and evaluated the drug for Spinal Muscular Atrophy 1.

Is AVXS-101 a monoclonal antibody?

Yes, AVXS-101 is classified as a monoclonal antibody. It is being developed for the treatment of Spinal Muscular Atrophy 1, a neurological condition. The drug is currently in Phase 1 clinical development.