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SION-719

Phase 2

Cystic Fibrosis (CF) | Small molecule | Respiratory |Sionna Therapeutics, Inc.|Last Updated: Sep 10, 2026

Target and mechanism

Molecular targetNBD1
Target classProtein
ModalitySmall molecule

Success Probability

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Market & Valuation

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Trial Design

RandomizedDouble-BlindCONTROLLEDDMC
Total Trials1
Total Enrollment16

FDA Designations

No designations recorded

Clinical trial landscape

SION-719 · 1 trial · 1 indication

Phase 2 1
NCT07108153Proof-of-concept Study to Evaluate the Safety, Tolerability, Pharmacodynamics, and Pharmacokinetics of SION-719 When Added to TrikaftaCystic Fibrosis (CF)
COMPLETED15 Analytics
PHASE2COMPLETED
Proof-of-concept Study to Evaluate the Safety, Tolerability, Pharmacodynamics, and Pharmacokinetics of SION-719 When Added to Trikafta
Cystic Fibrosis (CF)Unlock trial analytics

Study Endpoints

Primary Endpoints

To evaluate the incidence of treatment emergent adverse events [Safety and Tolerability] when SION-719 is administered to people with cystic fibrosis (CF) who are taking a standard stable dose of physician-prescribed Trikafta
Day 1 through day 57

Adverse events will be assessed by Common Terminology Criteria for Adverse Events (CTCAE), v. 5.0

Secondary Endpoints

Change from baseline in sweat chloride levels
Baseline to Day 15 in each treatment period
Concentration of SION-719 in plasma and change of concentration of SION-719 in plasma.
Day 1 through day 57
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Study Design & Arms

AllocationRANDOMIZED
MaskingQUADRUPLE
ModelCROSSOVER
PurposeTREATMENT

Treatment Arms

ArmTypeDescription
Crossover Treatment Sequence 1: SION-719 followed by placebo-to-match SION-719EXPERIMENTALParticipants receive SION-719 for one treatment period, and placebo to match SION-719 for the other treatment period. All participants will remain on their physician-prescribed Trikafta as background therapy throughout the study.
Crossover Treatment Sequence 2: Placebo-to-match SION-719 followed by SION-719EXPERIMENTALParticipants receive placebo to match SION-719 for one treatment period and SION-719 for the other treatment period. All participants will remain on their physician-prescribed Trikafta as background therapy throughout the study.

Interventions

NameTypeDescription
SION-719DRUGAll participants receive SION-719, as specified by their treatment sequence assignment
Placebo-to-match SION-719DRUGAll participants receive placebo to match SION-719, as specified by their treatment sequence assignment
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Eligibility Criteria

Age Range18 Years to 65 Years
SexALL
Healthy VolunteersNo
Study Sites13

Inclusion Criteria: * Diagnosis of CF with F508del homozygous genotype based on documented CFTR genotype laboratory report. * Adherent to physician-prescribed Trikafta, as assessed by the Investigator, for at least 3 months prior to the Screening visit, taken at the recommended dose without modific...

Countries:United StatesAustralia
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Competitive Landscape -Cystic Fibrosis 17 trials (matched to "Cystic Fibrosis (CF)")

Recent Changes (Last 90 Days)

HIGHSep 10, 2026NCT07108153Status: ACTIVE_NOT_RECRUITING → COMPLETED
HIGHSep 10, 2026NCT07108153Status: ACTIVE_NOT_RECRUITING → COMPLETED

Frequently asked questions about SION-719

What is SION-719?

SION-719 is an investigational small molecule being developed by Sionna Therapeutics for the treatment of cystic fibrosis. It is designed to be used as an add-on therapy in people with CF and is currently in Phase 2 clinical development. It has not been approved by the FDA.

What is SION-719 used for in cystic fibrosis?

SION-719 is being studied for cystic fibrosis, a respiratory disease. The Phase 2 proof-of-concept trial evaluated SION-719 when added to Trikafta in adults with CF. It is an investigational therapy and is not approved for any indication.

What does SION-719 target?

SION-719 targets NBD1, the nucleotide-binding domain 1 of the cystic fibrosis transmembrane conductance regulator protein. NBD1 is a protein target, and SION-719 is a small molecule designed to act on it. This mechanism is being explored as an add-on approach in cystic fibrosis.

Who is developing SION-719?

SION-719 is being developed by Sionna Therapeutics, Inc., which trades on the Nasdaq under the ticker SION. The company is advancing the compound for cystic fibrosis.

What phase is SION-719 in?

SION-719 is in Phase 2 clinical development. It is an investigational drug and has not been approved by the FDA. The Phase 2 proof-of-concept study has been completed, and no Phase 3 trials for SION-719 have been registered.

What clinical trials is SION-719 in?

SION-719 has been studied in one clinical trial, NCT07108153, a Phase 2 proof-of-concept study evaluating its safety, tolerability, pharmacodynamics, and pharmacokinetics when added to Trikafta. The trial enrolled 15 participants across the United States and Australia and has been completed.