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OCU400 Low Dose

Phase 1

Retinitis Pigmentosa | Small molecule | Rare Disease |Ocugen, Inc.|Last Updated: Jul 31, 2026

Target and mechanism

Molecular targetNR2E3
ModalitySmall molecule

Success Probability

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Market & Valuation

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Trial Design

NO_TREATMENT_CONTROLLEDDMC
Total Trials1
Total Enrollment22

FDA Designations

RMAT

Clinical trial landscape

OCU400 Low Dose · 1 trial · 2 indications

Phase 1 1
NCT05203939Study to Assess the Safety and Efficacy of OCU400 for Retinitis Pigmentosa and Leber Congenital AmaurosisRetinitis Pigmentosa
ACTIVE NOT_RECRUITING22 Analytics
PHASE1ACTIVE NOT_RECRUITING
Study to Assess the Safety and Efficacy of OCU400 for Retinitis Pigmentosa and Leber Congenital Amaurosis
Retinitis PigmentosaUnlock trial analytics

Study Endpoints

Primary Endpoints

Study Drug-related adverse events (SDAE)
1 year

Counts, frequencies and percentages of SDAEs. SDAE is a primary adverse event of interest and defined as AEs and SAEs that are direct subjects to the Study Drug only.

Treatment-Emergent adverse events (TEAEs)
1 year

Counts, frequencies and percentages TEAEs. TEAEs are defined as an event that was not present prior to administration of the dose of study drug and present after the dose, or if it represents the exacerbation of an event that was present prior to the dose.

Serious adverse events (SAEs)
1 year

Counts, frequencies and percentages of SAEs including Resulted in Death, Life-threatening, Hospitalization, Disabling/incapacitating, Congenital anomaly or birth defect and medically significant AEs ( AE that did not meet any of the above criteria but could have jeopardized the subject and might have required medical or surgical intervention to prevent one of the outcomes listed above).

Secondary Endpoints

Best-corrected visual acuity (BCVA)
1 year (Changes from baseline)
Low-luminance visual acuity (LLVA)
1 year (Changes from baseline)
Slit-lamp biomicroscopy
1 year (Changes from baseline)
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Study Design & Arms

AllocationNON_RANDOMIZED
MaskingNONE
ModelSEQUENTIAL
PurposeTREATMENT

Treatment Arms

ArmTypeDescription
Cohort 1 (Low Dose)EXPERIMENTALBiallelic autosomal recessive NR2E3 mutations subgroup or Autosomal dominant NR2E3 mutation or RHO mutations subgroup
Cohort 2 (Mid Dose)EXPERIMENTALBiallelic autosomal recessive NR2E3 mutations subgroup or Autosomal dominant NR2E3 mutation or RHO mutations subgroup
Cohort 3 (High Dose)EXPERIMENTALBiallelic autosomal recessive NR2E3 mutations subgroup or Autosomal dominant NR2E3 mutation, RHO mutations subgroup
Pediatric ArmEXPERIMENTALPediatric subjects will receive the medium dose concentration
Phase 2 (High and Medium Dose)EXPERIMENTALFollowing DSMB confirmation, adult RP subjects with Biallelic autosomal recessive NR2E3 mutations, autosomal dominant NR2E3 mutations, Autosomal dominant RHO mutations will receive a high dose concentration of OCU400 or LCA patients with CEP290 mutation will receive a medium dose concentration of OCU400.
Adult ArmEXPERIMENTALBiallelic autosomal recessive NR2E3 mutations subgroup or Autosomal dominant NR2E3 mutation, RHO mutations subgroup will receive a high dose concentration of OCU400 and LCA patients with CEP290 will receive a medium dose concentration of OCU400
Second Eye DosingEXPERIMENTALEligible RP participants will be dosed in the untreated fellow eye with a therapeutic dose used in Phase 3 study of OCU400 (1.0x10E11vg/mL in 250 μl ) and will be followed for an additional 48 weeks.
Natural History Study (OCU400-104)NO_INTERVENTIONA Prospective and Retrospective Natural History Study of RP and LCA: This is an observatory study for the prospective natural history of RP and LCA in adult and pediatric subjects. The study will also collect and review retrospective data and ophthalmology examination of natural history and progression of disease for all subjects starting with earliest timepoint on or after the date of their diagnosis of RP or LCA. Subjects will be seen up to a total of four times during the 12 months of the Observational Period, at baseline, 3 months, 6 months and 12 months. A total of up to 100 subjects will be enrolled in the study, including: Approximately 76 newly enrolled subjects consisting of 50 adult RP subjects, 6 adult LCA subjects, 20 pediatric RP/LCA subjects. Up to 24 subjects that reconsent from the OCU400-101 study (subjects from OCU400-101 will provide data on their untreated eye)

Interventions

NameTypeDescription
OCU400 Low DoseDRUGsubretinal injection of up to 1.66×10E10 vg/mL
OCU400 Med DoseDRUGsubretinal injection of up to 3.33×10E10 vg/mL
OCU400 High DoseDRUGsubretinal injection of up to 1.66×10E11 vg/mL
OCU400 Second Eye DosingDRUGsubretinal injection of 1.0x10E11vg/mL in 250 μl
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Eligibility Criteria

Age Range6 Years to N/A
SexALL
Healthy VolunteersNo
Study Sites7

Diagnosis and main criteria for inclusion: Subjects meeting all inclusion criteria and none of the exclusion criteria are eligible for study participation. Inclusion Criteria for Adult RP: 1. Males or females ≥ 18 years of age at the time of informed consent. 2. Confirmed genetic diagnosis of bia...

Countries:United States
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Recent Changes (Last 90 Days)

LOWJul 31, 2026NCT05203939lastUpdatePostDate: changed
LOWJul 31, 2026NCT05203939lastUpdatePostDate: changed

Frequently asked questions about OCU400 Low Dose

What is OCU400 Low Dose used for in Retinitis Pigmentosa?

OCU400 Low Dose is an investigational small molecule being developed for the treatment of Retinitis Pigmentosa, a rare inherited retinal disease. It is currently in Phase 1 clinical development and has not been approved by the FDA. The drug is also being studied in patients with Leber Congenital Amaurosis.

What does OCU400 Low Dose target?

OCU400 Low Dose targets the NR2E3 receptor, a nuclear receptor involved in retinal cell function and survival. By modulating this target, the drug aims to address the underlying genetic causes of Retinitis Pigmentosa and potentially slow or halt disease progression.

Who makes OCU400 Low Dose?

OCU400 Low Dose is being developed by Ocugen, Inc., a biopharmaceutical company traded on the Nasdaq under the ticker symbol OCGN. Ocugen is conducting clinical research on this drug candidate for rare retinal diseases.

What phase is OCU400 Low Dose in?

OCU400 Low Dose is in Phase 1 clinical development. It is an investigational drug and has not received FDA approval. The ongoing Phase 1 trial is active but not recruiting participants, and the drug has been granted Regenerative Medicine Advanced Therapy (RMAT) designation by the FDA.

What clinical trials is OCU400 Low Dose in?

OCU400 Low Dose is being evaluated in a single Phase 1 clinical trial with the identifier NCT05203939. This trial is titled 'Study to Assess the Safety and Efficacy of OCU400 for Retinitis Pigmentosa and Leber Congenital Amaurosis' and is enrolling 22 participants in the United States.

Is OCU400 Low Dose the same as OCU400?

OCU400 Low Dose is a specific dosage form of the drug candidate OCU400, which is being developed by Ocugen. The clinical trial NCT05203939 evaluates OCU400 in patients with Retinitis Pigmentosa and Leber Congenital Amaurosis, and the low dose formulation is part of this broader development program.