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Revusiran

Phase 3

Transthyretin (TTR) Mediated Familial Amyloidotic Cardiomyopathy (FAC) | Small molecule | Neurology |Alnylam Pharmaceuticals, Inc.|Last Updated: Jul 18, 2018

Success Probability
Approval Probability 71%
TA Base Rate26%
Adjusted LOA41%
ML RiskLOW_RISK
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Market & Valuation
rNPV $3.2B
Market Size $9.4B
Revenue Basis $1.6B
Competitors 6
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Trial Design
RandomizedDouble-BlindPLACEBO_CONTROLLEDDMCBiomarker
Total Trials1
Total Enrollment206
FDA Designations
No designations recorded
Clinical Trials (1)
NCT IDTitlePhaseStatusEnrollmentVelocityDesignStartCompletionLast UpdatedSitesCountries
NCT02319005ENDEAVOUR: Phase 3 Multicenter Study of Revusiran (ALN-TTRSC) in Patients With Transthyretin (TTR) Mediated Familial Amyloidotic Cardiomyopathy (FAC)PHASE3 COMPLETED 206Dec 1, 2014Mar 30, 2017Jul 18, 201861 United States, Belgium +7
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Study Endpoints
Primary Endpoints
6 Minute Walk Distance (6-MWD)
18 months

The difference between revusiran and placebo group in change from baseline to 18 months in the total distance walked in 6 minutes

Serum TTR Levels
18 months

The difference between revusiran (ALN-TTRSC) and placebo group in the percent reduction in serum TTR levels over 18 months

Secondary Endpoints
Composite Cardiovascular (CV) Mortality and Cardiovascular (CV) Hospitalization
18 months
New York Heart Association (NYHA) Class
18 months
Kansas City Cardiomyopathy Questionnaire (KCCQ)
18 months
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Study Design & Arms
AllocationRANDOMIZED
MaskingDOUBLE
ModelPARALLEL
PurposeTREATMENT
Treatment Arms
ArmTypeDescription
Revusiran (ALN-TTRSC)ACTIVE_COMPARATORadministered by subcutaneous (SC) injection
Sterile Normal Saline (0.9% NaCl)PLACEBO_COMPARATORadministered by subcutaneous (SC) injection
Interventions
NameTypeDescription
Revusiran (ALN-TTRSC)DRUG -
Sterile Normal Saline (0.9% NaCl)DRUG -
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Eligibility Criteria
Age Range18 Years — 90 Years
SexALL
Healthy VolunteersNo
Study Sites61

Inclusion Criteria: * Documented TTR mutation * Amyloid deposits in cardiac or non-cardiac tissue * Medical history of heart failure * Evidence of cardiac involvement by echocardiogram Exclusion Criteria: * Has known primary amyloidosis (AL), leptomeningeal amyloidosis, non-FAC hereditary cardiom...

Countries:United StatesBelgiumCanadaFranceGermanyItalySpainSwedenUnited Kingdom
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