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Nexiguran ziclumeran

Phase 3

Neuromuscular Disease | Monoclonal antibody | Rare Disease |Intellia Therapeutics, Inc.|Last Updated: Apr 16, 2026

Target and mechanism

Molecular targetTTR
ModalityMonoclonal antibody

Also known as NTLA-2001

Success Probability

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Market & Valuation

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Trial Design

RandomizedDouble-BlindPLACEBO_CONTROLLEDDMC
Total Trials1
Total Enrollment60

FDA Designations

RMATORPHAN_DRUG

Clinical trial landscape

Nexiguran ziclumeran · 3 trials · 24 indications

Phase 3 2Phase 1 1
NCT06672237A Phase 3 Study of NTLA-2001 in ATTRv-PNNeuromuscular Disease
RECRUITING60 Analytics
NCT06128629MAGNITUDE: A Phase 3 Study of NTLA-2001 in Participants With Transthyretin Amyloidosis With Cardiomyopathy (ATTR-CM)Transthyretin Amyloidosis (ATTR) With Cardiomyopathy
RECRUITING1,200 Analytics
PHASE3RECRUITING
A Phase 3 Study of NTLA-2001 in ATTRv-PN
Neuromuscular DiseaseUnlock trial analytics
PHASE3RECRUITING
MAGNITUDE: A Phase 3 Study of NTLA-2001 in Participants With Transthyretin Amyloidosis With Cardiomyopathy (ATTR-CM)
Transthyretin Amyloidosis (ATTR) With CardiomyopathyUnlock trial analytics

Study Endpoints

Primary Endpoints

Modified Neuropathy Impairment Score +7 (mNIS+7)
18 Months
Serum TTR
29 Days
Composite outcome of cardiovascular (CV) mortality and CV events
Maximum study duration is dependent on event rates and is estimated to be at least 18 months and up to approximately 5 years
Number of Participants with Treatment-Emergent Adverse Events
up to Day 730
Number of Participants with Clinically Significant Clinical Laboratory Test Findings
up to Day 730
Number of Participants with Clinically Significant Safety Measurements
up to Day 730
Percent Change from Baseline in Serum TTR (enzyme-linked immunosorbent assay [ELISA])
up to Day 730
Percent Change from Baseline in Serum Prealbumin
up to Day 730
Mean Area Under the Plasma Concentration-Time Curve from Time Zero to the Time of the Last Measurable Concentration (AUClast) for DMG-PEG2k, LP000001, Cas9 mRNA, and sgRNA
up to Day 730
Mean Area Under the Plasma Concentration-Time Curve from Time Zero to Infinity (AUCinf) for DMG-PEG2k, LP000001, Cas9 mRNA, and sgRNA
up to Day 730
Mean Maximum Concentration (Cmax) for DMG-PEG2k, LP000001, Cas9 mRNA, and sgRNA
up to Day 730
Mean Time of the Maximum Concentration (Tmax) for DMG-PEG2k, LP000001, Cas9 mRNA, and sgRNA
up to Day 730
Mean Terminal Half-Life (t½) for DMG-PEG2k, LP000001, Cas9 mRNA, and sgRNA
up to Day 730
Mean Apparent Clearance (CL) for DMG-PEG2k, LP000001, Cas9 mRNA, and sgRNA
up to Day 730
Mean Volume of Distribution (Vd) for DMG-PEG2k, LP000001, Cas9 mRNA, and sgRNA
up to Day 730
Change from Baseline in Anti-Drug Antibody to NTLA-2001 and Anti-Cas9 Protein Antibody to Transgene Product Levels
up to Day 730

Secondary Endpoints

Norfolk Quality of Life-Diabetic Neuropathy (Norfolk QoL-DN) Questionnaire
18 Months
Modified Body Mass Index (mBMI)
18 Months
Serum TTR
18 Months
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Study Design & Arms

AllocationRANDOMIZED
MaskingQUADRUPLE
ModelPARALLEL
PurposeTREATMENT

Treatment Arms

ArmTypeDescription
nexiguran ziclumeranEXPERIMENTALnexiguran ziclumeran 55 mg by single IV infusion
Normal SalinePLACEBO_COMPARATORPlacebo; Normal saline (0.9% NaCl) by single IV infusion
NTLA-2001EXPERIMENTALSingle intravenous (IV) infusion of NTLA-2001
PlaceboPLACEBO_COMPARATORSingle IV infusion of normal saline
Polyneuropathy Part 1: NTLA-2001EXPERIMENTALParticipants, assigned to one of 4 dose-escalation cohorts, will receive a single dose of NTLA-2001.
Polyneuropathy Part 2: NTLA-2001EXPERIMENTALParticipants, assigned to the dose-expansion cohort, will receive a single dose of NTLA-2001.
Cardiomyopathy Part 1 (UK only): NTLA-2001EXPERIMENTALParticipants, assigned to one of 2 dose-escalation cohorts, will receive a single dose of NTLA-2001.
Cardiomyopathy Part 2 (UK only): NTLA-2001EXPERIMENTALParticipants, assigned to the dose-expansion cohort, will receive a single dose of NTLA-2001.
Polyneuropathy Follow-on Dosing (PN Part 1 Dose Level 1 Subjects only): NTLA-2001EXPERIMENTALParticipants assigned to the follow-on dosing cohort will receive a subsequent dose of NTLA-2001.

Interventions

NameTypeDescription
nexiguran ziclumeranBIOLOGICALnexiguran ziclumeran 55 mg by single IV infusion
Normal Saline as PlaceboDRUGNormal saline (0.9% NaCl) by single IV infusion
NTLA-2001BIOLOGICALNTLA-2001 (55mg) by IV infusion
PlaceboDRUGNormal saline (0.9% NaCl) by IV infusion
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Eligibility Criteria

Age Range18 Years to 85 Years
SexALL
Healthy VolunteersNo
Study Sites14

Inclusion Criteria: * Diagnosis of ATTRv-PN * Karnofsky Performance Status (KPS) ≥ 60 Exclusion Criteria: * Other causes of amyloidosis (amyloidosis caused by non-TTR protein) * Other known causes of sensorimotor or autonomic neuropathy * Diabetes mellitus * New York Heart Association Class III o...

Countries:ArgentinaBrazilMexicoSingaporeTaiwanThailandUnited StatesAustraliaAustriaBelgiumCanadaCzechiaDenmarkFranceGermanyHungaryIsraelItalyJapanNetherlandsNew ZealandNorwayPortugalSouth KoreaSpainSwedenUnited Kingdom
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Frequently asked questions about Nexiguran ziclumeran

What is nexiguran ziclumeran used for?

Nexiguran ziclumeran is an investigational therapy being developed for the treatment of hereditary transthyretin amyloidosis with polyneuropathy (ATTRv-PN), a form of neuromuscular disease. It is currently in Phase 3 clinical development and has not been approved by regulatory authorities.

What does nexiguran ziclumeran target?

Nexiguran ziclumeran targets the transthyretin (TTR) protein. By targeting TTR, the therapy is designed to address the underlying cause of hereditary transthyretin amyloidosis with polyneuropathy, a condition in which abnormal TTR protein accumulates and damages nerves.

Who is developing nexiguran ziclumeran?

Nexiguran ziclumeran is being developed by Intellia Therapeutics, Inc., a biotechnology company traded on NASDAQ under the ticker symbol NTLA. The company is conducting a Phase 3 clinical trial of the therapy in patients with hereditary transthyretin amyloidosis with polyneuropathy.

What phase is nexiguran ziclumeran in?

Nexiguran ziclumeran is in Phase 3 clinical development. It is an investigational therapy and has not been approved by the FDA. The drug has received Regenerative Medicine Advanced Therapy (RMAT) designation and Orphan Drug designation from the FDA.

What clinical trials is nexiguran ziclumeran in?

Nexiguran ziclumeran is being studied in a Phase 3 clinical trial registered as NCT06672237. This randomized, double-blind, placebo-controlled study is recruiting 60 participants aged 18 years and older with hereditary transthyretin amyloidosis with polyneuropathy. The trial is being conducted in Argentina, Brazil, Mexico, Singapore, Taiwan, and Thailand.

Is nexiguran ziclumeran the same as NTLA-2001?

Yes, nexiguran ziclumeran is also known as NTLA-2001. The Phase 3 clinical trial NCT06672237 is titled 'A Phase 3 Study of NTLA-2001 in ATTRv-PN,' confirming that the drug is being evaluated under this alternative name in clinical research.