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Avacopan

Phase 3

ANCA-Associated Vasculitis | Small molecule | Immunology |Amgen Inc.|Last Updated: Jul 20, 2026

Target and mechanism

Molecular targetC5AR1
Target classAntagonist
ModalitySmall molecule

Success Probability

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Market & Valuation

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Trial Design

RandomizedDouble-BlindACTIVE_CONTROLLEDDMC
Total Trials1
Total Enrollment331

FDA Designations

No designations recorded

Clinical trial landscape

Avacopan · 9 trials · 12 indications

Phase 3 2Phase 2 3Phase 1 4
NCT06321601Study to Evaluate Avacopan in Combination With a Rituximab or Cyclophosphamide-containing Regimen, in Children From 6 Years to < 18 Years of Age With AAV.Vasculitis
ACTIVE NOT_RECRUITING19 Analytics
NCT02994927A Phase 3 Clinical Trial of CCX168 (Avacopan) in Patients With ANCA-Associated VasculitisANCA-Associated Vasculitis
COMPLETED331 Analytics
PHASE3ACTIVE NOT_RECRUITING
Study to Evaluate Avacopan in Combination With a Rituximab or Cyclophosphamide-containing Regimen, in Children From 6 Years to < 18 Years of Age With AAV.
VasculitisUnlock trial analytics
PHASE3COMPLETED
A Phase 3 Clinical Trial of CCX168 (Avacopan) in Patients With ANCA-Associated Vasculitis
ANCA-Associated VasculitisUnlock trial analytics

Study Endpoints

Primary Endpoints

Proportion of Participants Achieving Disease Remission at Week 26 According to the Pediatric Vasculitis Activities Score (PVAS)
Week 26
Proportion of Participants With Sustained Disease Remission at Week 52 According to the PVAS
Week 52
Percentage of Subjects Achieving Disease Remission at Week 26
Week 26

Disease remission at Week 26 was defined as: * Achieving a BVAS of 0 as determined by the Adjudication Committee; * No administration of glucocorticoids given for ANCA-associated vasculitis within 4 weeks prior to Week 26; * No BVAS \>0 during the 4 weeks prior to Week 26 (if collected for an unscheduled assessment).

Percentage of Subjects Achieving Sustained Disease Remission at Week 52
Week 52

Sustained remission at Week 52 was defined as: * Disease remission at Week 26 as defined above; * Disease remission at Week 52 defined as a BVAS of 0 at Week 52 as determined by the Adjudication Committee and no administration of glucocorticoids for treatment of ANCA-associated vasculitis within 4 weeks prior to Week 52; * No disease relapse between Week 26 and Week 52 as determined by the Adjudication Committee.

Proportion of patients in ENT remission without relapse
Week 52

The proportion of patients in ENT remission without relapse in each treatment group at week 52 with no glucocorticoid (GC) exposure 4 weeks prior to week 52, where ENT remission is defined as a score of 0 on GPA ENT disease activity score

Percentage of Subjects Achieving Hidradenitis Suppurativa Clinical Response (HiSCR) at Week 12.
Baseline to Week 12

The percentage of subjects achieving Hidradenitis Suppurativa Clinical Response (HiSCR) at Week 12 in the ITT1 population using the NRI-CMH Test. A response was defined as a reduction of at least 50 in abscess and inflammatory nodule (AN) count with no increase in abscess count and no increase in draining fistula count compared with baseline. The ITT1 population was defined as all subjects who were randomized at baseline and received at least 1 dose of investigational product during period 1. NRI- non-responder imputation; CMH- Cochran-Mantel-Haenszel. Percentage values have been reported as opposed to proportion values to allow for statistical analyses.

Change From Baseline to Week 26 in the C3G Histologic Index for Disease Activity - Subjects With Elevated C5b-9
Week 26

Change from baseline to Week 26 in the biopsy-based C3G Histologic Index for disease activity - Subjects with Elevated C5b-9 (\> 244 ng/mL) in the Intent-to-Treat Population. C3G Histological Index for Disease Activity Scores can range from 0 to 21. A decrease indicates improvement. C3G=C3 glomerulopathy

Percent Change From Baseline to Week 26 in the C3G Histologic Index for Disease Activity - Combined C5b-9 Strata
Week 26

Percent change from baseline to Week 26 in the biopsy-based C3G Histologic Index for disease activity - Combined C5b-9 Strata (elevated \[\> 244 ng/mL\] and non-elevated C5b-9) in the Intent-to-Treat Population. C3G Histological Index for Disease Activity Scores can range from 0 to 21. A decrease indicates improvement. C3G=C3 glomerulopathy \* Multiple Imputation: Missing Week 26 values are imputed using the regression method to create 100 complete datasets.

Maximum Observed Plasma Concentration (Cmax) of Avacopan
Group 1, Period 1: predose, 0.25,0.5,1,2,3,4,6,9,12,16,24,36 hours, Days 3,4,5,6,7,8,12,15, and 18 postdose; Group 2, Periods 1 and 2: predose, 0.25,0.5,1,2,3,4,6,9,12,16,24,36 hours, Days 3,4,5,6,7,8,12,15, and 18 postdose

Cmax was obtained using noncompartmental analysis.

Cmax of Metabolite M1
Group 1, Period 1: predose, 0.25,0.5,1,2,3,4,6,9,12,16,24,36 hours, Days 3,4,5,6,7,8,12,15, and 18 postdose; Group 2, Periods 1 and 2: predose, 0.25,0.5,1,2,3,4,6,9,12,16,24,36 hours, Days 3,4,5,6,7,8,12,15, and 18 postdose

Cmax was obtained using noncompartmental analysis.

Area Under the Plasma Concentration-time Curve (AUC) From Time Zero to Time of Last Quantifiable Concentration (AUClast) of Avacopan
Group 1, Period 1: predose, 0.25,0.5,1,2,3,4,6,9,12,16,24,36 hours, Days 3,4,5,6,7,8,12,15, and 18 postdose; Group 2, Periods 1 and 2: predose, 0.25,0.5,1,2,3,4,6,9,12,16,24,36 hours, Days 3,4,5,6,7,8,12,15, and 18 postdose

AUClast was obtained using noncompartmental analysis.

AUClast of Metabolite M1
Group 1, Period 1: predose, 0.25,0.5,1,2,3,4,6,9,12,16,24,36 hours, Days 3,4,5,6,7,8,12,15, and 18 postdose; Group 2, Periods 1 and 2: predose, 0.25,0.5,1,2,3,4,6,9,12,16,24,36 hours, Days 3,4,5,6,7,8,12,15, and 18 postdose

AUClast was obtained using noncompartmental analysis.

AUC From Time Zero to Infinity (AUCinf) of Avacopan
Group 1, Period 1: predose, 0.25,0.5,1,2,3,4,6,9,12,16,24,36 hours, Days 3,4,5,6,7,8,12,15, and 18 postdose; Group 2, Periods 1 and 2: predose, 0.25,0.5,1,2,3,4,6,9,12,16,24,36 hours, Days 3,4,5,6,7,8,12,15, and 18 postdose

AUCinf was obtained using noncompartmental analysis.

AUCinf of Metabolite M1
Group 1, Period 1: predose, 0.25,0.5,1,2,3,4,6,9,12,16,24,36 hours, Days 3,4,5,6,7,8,12,15, and 18 postdose; Group 2, Periods 1 and 2: predose, 0.25,0.5,1,2,3,4,6,9,12,16,24,36 hours, Days 3,4,5,6,7,8,12,15, and 18 postdose

AUCinf was obtained using noncompartmental analysis.

AUC From Time Zero to 48 Hours (AUC0-48) of Avacopan
Group 1, Period 1: predose, 0.25,0.5,1,2,3,4,6,9,12,16,24,36, and 48 hours postdose; Group 2, Periods 1 and 2: predose, 0.25,0.5,1,2,3,4,6,9,12,16,24,36, and 48 hours postdose

AUC0-48 was obtained using noncompartmental analysis.

AUC0-48 of Metabolite M1
Group 1, Period 1: predose, 0.25,0.5,1,2,3,4,6,9,12,16,24,36, and 48 hours postdose; Group 2, Periods 1 and 2: predose, 0.25,0.5,1,2,3,4,6,9,12,16,24,36, and 48 hours postdose

AUC0-48 was obtained using noncompartmental analysis.

Dialysate Clearance (CLD) of Avacopan
Group 2, Period 1: 0.5, 1, 2 and 3 hours after start of HD and after end of HD at Day 1

CLD determines how much of the drug is removed by hemodialysis.

CLD of Metabolite M1
Group 2, Period 1: 0.5, 1, 2 and 3 hours after start of HD and after end of HD at Day 1

CLD determines how much of the drug is removed by hemodialysis.

Maximum Observed Plasma Concentration (Cmax) of Simvastatin
Up to Day 12
Cmax of β-hydroxy-simvastatin Acid
Up to Day 12
Area Under the Plasma Concentration-time Curve from Time 0 to the Time Point of Last Quantifiable Plasma Concentration (AUClast) of Simvastatin
Up to Day 12
AUClast of β-hydroxy-simvastatin Acid
Up to Day 12
Area Under the Plasma Concentration-time Curve from Time 0 to Infinity (AUCinf) of Simvastatin
Up to Day 12
AUCinf of β-hydroxy-simvastatin Acid
Up to Day 12
Change from Baseline in QTcF
Day -1 (baseline) and up to Day 14
Maximum Plasma Concentration (Cmax) of Avacopan
Up to Day 18
Cmax of CCX168-M1
Up to Day 18
Time of Cmax (Tmax) of Avacopan
Up to Day 18
Tmax of CCX168-M1
Up to Day 18
Terminal Phase Rate Constant of Avacopan
Up to Day 18
Terminal Phase Rate Constant of CCX168-M1
Up to Day 18
Apparent Terminal Half-life (t1/2z) of Avacopan
Up to Day 18
t1/2z of CCX168-M1
Up to Day 18
Apparent Oral Clearance (CL/F) of Avacopan
Up to Day 18
CL/F of CCX168-M1
Up to Day 18
Apparent Volume of Distribution (Vz/F) of Avacopan
Up to Day 18
Vz/F of CCX168-M1
Up to Day 18
Area Under the Plasma Concentration-time Curve (AUC) from Time 0 to Time t (time of last quantifiable plasma concentration) (AUClast) of Avacopan
Up to Day 18
AUClast of CCX168-M1
Up to Day 18
AUC from Time 0 to Time 6 Hours Post-dose (AUC0-6h) of Avacopan
Up to Hour 6
AUC0-6h of CCX168-M1
Up to Hour 6
AUC from Time 0 to Time 12 Hours Post-dose (AUC0-12h) of Avacopan
Up to Hour 12
AUC0-12h of CCX168-M1
Up to Hour 12
AUC from Time 0 to Infinity (AUC0-inf) of Avacopan
Up to Day 18
AUC0-inf of CCX168-M1
Up to Day 18

Secondary Endpoints

Plasma Concentrations of Avacopan
Day 1 up to Week 52
Number of Participants Experiencing Treatment-emergent Adverse Events (TEAE)
Day 1 up to approximately Week 60
Proportion of Participants Achieving Disease Remission at Week 26 According to the Birmingham Vasculitis Activity Score (BVAS)
Week 26
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Study Design & Arms

AllocationNON_RANDOMIZED
MaskingNONE
ModelSINGLE_GROUP
PurposeTREATMENT

Treatment Arms

ArmTypeDescription
AvacopanEXPERIMENTALParticipants will receive avacopan twice-daily (BID) administered as oral tablets or liquid formula for 52 weeks.
Prednisone groupACTIVE_COMPARATORAvacopan-matching placebo plus cyclophosphamide/azathioprine or rituximab plus a full starting dose of prednisone.
Avacopan groupEXPERIMENTALAvacopan plus cyclophosphamide/azathioprine or rituximab plus prednisone-matching placebo.
TAVNEOSACTIVE_COMPARATORBID dose of 30 mg TAVNEOS
PlaceboPLACEBO_COMPARATORBID dose of 30 mg TAVNEOS-matching placebo
Group APLACEBO_COMPARATORPlacebo twice daily (BID) for Period 1 of the study
Group BEXPERIMENTALAvacopan 10 mg twice daily (BID) for Period 1+2 of the study
Group CEXPERIMENTALAvacopan 30 mg twice daily (BID) for Period 1+2 of the study
Placebo to Avacopan 10 mgEXPERIMENTALTreatment period 2, subjects randomized to placebo during period 1 were rerandomized 1:1 to receive 10 mg or 30 mg avacopan BID in period 2.
Placebo to Avacopan 30 mgEXPERIMENTALTreatment period 2, subjects randomized to placebo during period 1 were rerandomized 1:1 to receive 10 mg or 30 mg avacopan BID in period 2.
Avacopan Matching PlaceboPLACEBO_COMPARATORMatching placebo capsules x 3 administered twice daily during the 26 week blinded treatment period period
Group 1: Normal Renal FunctionEXPERIMENTALParticipants in Group 1 will receive a single dose of avacopan on Day 1.
Group 2: ESRD Requiring HDEXPERIMENTALParticipants in Group 2 will receive a single dose of avacopan on Day 1 in each of 2 treatment periods (Period 1/on HD and Period 2/off HD).
Arm 1: Avacopan and SimvastatinEXPERIMENTALA single dose of 40 mg simvastatin will be given orally in the morning on Day 1 and Day 10. The Day 10 dose of simvastatin will be co-administered with the morning dose of avacopan. On Days 3 through 11, avacopan will be given orally at 30 mg BID.
Arm 2: Avacopan and SimvastatinEXPERIMENTALA single dose of 40 mg simvastatin will be given orally in the morning on Day 1 and Day 10. The Day 10 dose of simvastatin will be co-administered with the morning dose of avacopan. On Days 3 through 11, avacopan will be given orally at 60 mg BID.
Cohort 1: AvacopanEXPERIMENTALParticipants will be randomized to receive multiple doses of avacopan orally twice daily (BID): 30 mg for 7 days and 100 mg for 7 days, for a total of 14 dosing days, and placebo for moxifloxacin on Days 1 and 15.
Cohort 2A: Moxifloxacin/PlaceboACTIVE_COMPARATORParticipants will be randomized to receive moxifloxacin 400 mg orally on Day 1, placebo for avacopan BID on Days 1 to 14, and placebo for moxifloxacin on Day 15.
Cohort 2B: Placebo/MoxifloxacinACTIVE_COMPARATORParticipants will be randomized to receive placebo for moxifloxacin orally on Day 1, placebo for avacopan BID on Days 1 to 14, and moxifloxacin 400 mg orally on Day 15.
Group 1: Mild Hepatic ImpairmentEXPERIMENTALParticipants with mild hepatic impairment (defined using Child-Pugh Classification of the Severity of Liver Disease \[C-P\] criteria \[C-P Class A, score of 5 to 6 points\]) will receive a single oral dose of 30 mg avacopan on Day 1 in the fasted state.
Group 2: Moderate Hepatic ImpairmentEXPERIMENTALParticipants with moderate hepatic impairment (defined using the C-P criteria \[C-P Class B, score of 7 to 9 points\]) will receive a single oral dose of 30 mg avacopan on Day 1 in the fasted state.
Group 3: Healthy Control GroupACTIVE_COMPARATORParticipants with normal hepatic function (medically normal with no clinically significant illness or disease or abnormal physical examination findings, and with normal laboratory values at screening) will be demographically-matched to participants in Group 1 and Group 2, and will receive a single oral dose of 30 mg avacopan on Day 1 in the fasted state.

Interventions

NameTypeDescription
AvacopanDRUGOral administration
PrednisoneDRUGAvacopan-matching placebo twice daily orally for 52 weeks (364 days): \- Three avacopan-matching placebo capsules in the morning, preferably with food, and three in the evening, preferably with food, approximately 12 hours after the morning dose. Oral prednisone tapering regimen over 20 weeks (140 days): * Prednisone 60 mg per day if the subject's body weight was ≥55 kg, or 45 mg per day if the subject's body weight was \<55 kg, starting on Day 1 with tapering according to the protocol-specified schedule. * Adolescents who weighed ≤37 kg started at a prednisone dose of 30 mg per day.
CyclophosphamideDRUGOrally or intravenously administered
RituximabBIOLOGICALIntravenously administered
AzathioprineDRUGOrally administered
PlaceboDRUGBID dose of 30mg TAVNEOS-matching placebo (3-10mg capsules)
Avacopan Matching PlaceboDRUGavacopan matching placebo
SimvastatinDRUGOrally via tablets
MoxifloxacinDRUGAdministered orally.
Placebo for avacopanDRUGAdministered orally.
Placebo for moxifloxacinDRUGAdministered orally.
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Eligibility Criteria

Age Range6 Years to 17 Years
SexALL
Healthy VolunteersNo
Study Sites34

Inclusion Criteria: * Male and female children and adolescents from 6 to \< 18 years old of age. * Clinical diagnosis of Granulomatosis with Polyangiitis (GPA) or microscopic polyangiitis (MPA), consistent with Chapel-Hill Consensus Conference definitions (Jennette et al, 2013). * Positive anti-PR3...

Countries:United StatesBelgiumCanadaCzechiaFranceHungaryPolandSlovakiaSpainTurkey (Türkiye)AustraliaAustriaDenmarkGermanyIrelandItalyJapanNetherlandsNew ZealandNorwaySwedenSwitzerlandUnited Kingdom
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Recent Changes (Last 90 Days)

MEDIUMJul 20, 2026NCT06321601Status: RECRUITING → ACTIVE_NOT_RECRUITING
MEDIUMJul 20, 2026NCT06321601Status: RECRUITING → ACTIVE_NOT_RECRUITING
LOWJun 18, 2026NCT06321601lastUpdatePostDate: changed
LOWJun 18, 2026NCT06321601lastUpdatePostDate: changed
LOWJun 18, 2026NCT06321601lastUpdatePostDate: changed

Frequently asked questions about Avacopan

What is Avacopan used for?

Avacopan is an investigational small molecule being developed for ANCA-Associated Vasculitis, Hidradenitis Suppurativa, Vasculitis, Granulomatosis With Polyangiitis, and End-Stage Renal Disease (ESRD). It is also being studied in C3 Glomerulopathy and hepatic impairment. The drug is in Phase 3 clinical development for vasculitis indications.

Who makes Avacopan?

Avacopan is being developed by Amgen Inc., a biopharmaceutical company traded on the NASDAQ under the ticker symbol AMGN. The company is conducting clinical trials of Avacopan across multiple indications, including vasculitis and renal impairment, with studies in both adult and pediatric populations.

What phase is Avacopan in?

Avacopan is in Phase 3 clinical development for vasculitis, including a pediatric study in children aged 6 to under 18 years. It has also completed Phase 1 and Phase 2 trials for other conditions. The drug is investigational and not yet approved by regulatory authorities.

What clinical trials is Avacopan in?

Avacopan has been studied in several clinical trials. NCT03301467 was a completed Phase 2 trial in C3 Glomerulopathy with 57 participants. NCT06004934 was a completed Phase 1 pharmacokinetic study in hepatic impairment. NCT06321601 is an active Phase 3 trial in pediatric vasculitis. NCT06468826 was a completed Phase 1 study in ESRD.

Is Avacopan being studied in children?

Yes, Avacopan is being studied in children. NCT06321601 is an active Phase 3 trial evaluating Avacopan in combination with rituximab or cyclophosphamide-containing regimens in children aged 6 to under 18 years with vasculitis. This trial is currently active but not recruiting participants.

What is Avacopan's mechanism of action?

Avacopan is a small molecule immunology therapeutic. It targets the complement system, specifically the C5a receptor, to modulate inflammatory responses. This mechanism is relevant to its study in complement-mediated diseases like C3 Glomerulopathy and ANCA-Associated Vasculitis.