Recent Updates
Recently added Catalysts

AG-181

Phase 1

Phenylketonuria | Small molecule | Rare Disease |Agios Pharmaceuticals, Inc.|Last Updated: May 29, 2026

Success Probability
Approval Probability 71%
TA Base Rate26%
Adjusted LOA41%
ML RiskLOW_RISK
Premium
Market & Valuation
rNPV $3.2B
Market Size $9.4B
Revenue Basis $1.6B
Competitors 6
Premium
Trial Design
CONTROLLEDBiomarker
Total Trials1
Total Enrollment20
FDA Designations
No designations recorded
Clinical Trials (1)
NCT IDTitlePhaseStatusEnrollmentVelocityDesignStartCompletionLast UpdatedSitesCountries
NCT07241234A Study to Evaluate Safety, Tolerability, Pharmacokinetics, and Pharmacodynamics of AG-181 in Subjects With PhenylketonuriaPHASE1 RECRUITING 20Apr 17, 2026Jan 17, 2028May 29, 20262 United States, Poland
Unlock Drug Trial Details
Study Endpoints
Primary Endpoints
Number of Subjects with Adverse Events (AEs) and Serious Adverse Events (SAEs) by Type, Severity, and Relationship to the Study Drug
Up to Day 42
Secondary Endpoints
Plasma Concentration of AG-181
Up to Day 28
Maximum Concentration (Cmax) of AG-181
Up to Day 28
Time to Maximum (Peak) Concentration (Tmax) of AG-181
Up to Day 28
Unlock Study Endpoints
Study Design & Arms
AllocationNON_RANDOMIZED
MaskingNONE
ModelSEQUENTIAL
PurposeTREATMENT
Treatment Arms
ArmTypeDescription
Cohort 1: AG-181EXPERIMENTALSubjects will receive AG-181 from Day 1 to Day 28.
Cohort 2 (Optional Cohort): AG-181EXPERIMENTALSubjects will receive AG-181.
Interventions
NameTypeDescription
AG-181DRUGAG-181 film-coated tablets
Unlock Study Design Details
Eligibility Criteria
Age Range18 Years — 69 Years
SexALL
Healthy VolunteersNo
Study Sites2

Key Inclusion Criteria: * Diagnosis of PKU, defined as documented presence of 2 mutant alleles in the phenylalanine hydroxylase (PAH) gene, of which at least 1 is the R408W mutation, as determined during Screening per the genotyping performed by the study central genotyping laboratory. * At least 1...

Countries:United StatesPoland
Unlock Eligibility Criteria
Competitive Landscape -Phenylketonuria 12 trials
Recent Changes (Last 90 Days)
LOWMay 29, 2026NCT07241234startDate: changed
LOWMay 29, 2026NCT07241234startDate: changed
LOWMay 29, 2026NCT07241234startDate: changed
LOWMay 26, 2026NCT07241234Status: NOT_YET_RECRUITING → RECRUITING
LOWMay 24, 2026NCT07241234studyFirstPostDate: changed