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phenylbutyrate

Phase 2

Medium-chain Acyl-CoA Dehydrogenase Deficiency | Small molecule | Other |Zevra Therapeutics, Inc.|Last Updated: Jul 11, 2025

Success Probability
Approval Probability 71%
TA Base Rate26%
Adjusted LOA41%
ML RiskLOW_RISK
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Market & Valuation
rNPV $3.2B
Market Size $9.4B
Revenue Basis $1.6B
Competitors 6
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Trial Design
UNCONTROLLEDBiomarker
Total Trials1
Total Enrollment24
FDA Designations
No designations recorded
Clinical Trials (1)
NCT IDTitlePhaseStatusEnrollmentVelocityDesignStartCompletionLast UpdatedSitesCountries
NCT06773026Study of Sodium Phenylbutyrate (ACER-001) for the Treatment of Pediatric and Adults Patients With Medium Chain Acyl-CoA Dehydrogenase Deficiency (MCADD)PHASE2 RECRUITING 24Jun 30, 2025Jul 1, 2027Jul 11, 20251 United States
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Study Endpoints
Primary Endpoints
Number of participants with treatment related adverse events as assessed by CTCAE v5.0
5 weeks
Secondary Endpoints
Length of time before glucose falls below 60 mg/dL
5 weeks
Length of time before glucose falls below 70 mg/dL
5 weeks
Length of time before glucose falls below 80 mg/dL
5 weeks
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Study Design & Arms
AllocationNA
MaskingNONE
ModelSINGLE_GROUP
PurposeTREATMENT
Treatment Arms
ArmTypeDescription
4.0 g/m2/day BID sodium phenylbutyrateEXPERIMENTALUp to 24 subjects (12: ages 4-9 years old; 12:10 years of age and older) will be randomized to take 4.0 g/m2/day divided into two daily doses
Interventions
NameTypeDescription
Sodium phenylbutyrateDRUGOpen-label design with doses of sodium phenylbutyrate at 4.0 g/m2/day
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Eligibility Criteria
Age Range4 Years — N/A
SexALL
Healthy VolunteersNo
Study Sites1

Inclusion Criteria: 1. A diagnosis of MCADD and molecular confirmation of at least one copy of the common c.985A\>G mutation. 2. ≥4 years of age 3. Able to perform and comply with study activities placement of a continuous glucose monitor, IV catheter, and all blood draws. 4. Negative pregnancy tes...

Countries:United States
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Recent Changes (Last 90 Days)
LOWMay 24, 2026NCT06773026studyFirstPostDate: changed