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TSHA-101

Phase 1

Infantile GM2 Gangliosidosis (Disorder) | Monoclonal antibody | Rare Disease |Taysha Gene Therapies, Inc.|Last Updated: May 9, 2023

Success Probability
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Market & Valuation
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Trial Design
UNCONTROLLEDDMC
Total Trials1
Total Enrollment3
FDA Designations
No designations recorded
Clinical trial landscape

TSHA-101 · 1 trial · 1 indication

Phase 1 1
NCT04798235First-in-Human Study of TSHA-101 Gene Therapy for Treatment of Infantile Onset GM2 GangliosidosisInfantile GM2 Gangliosidosis (Disorder)
ACTIVE NOT_RECRUITING3 Analytics
PHASE1ACTIVE NOT_RECRUITING
First-in-Human Study of TSHA-101 Gene Therapy for Treatment of Infantile Onset GM2 Gangliosidosis
Infantile GM2 Gangliosidosis (Disorder)Unlock trial analytics
Study Endpoints
Primary Endpoints
Safety and tolerability: Treatment-emergent Adverse Events (TEAEs)
1 year

Incidence, severity, and relatedness of TEAEs

Safety and Tolerability: Number of participants with abnormal Laboratory assessments
1 year

Number of participants with Changes from Baseline in laboratory assessments

Safety and Tolerability: Electrocardiogram (ECG)
1 year

Changes from Baseline in 12-lead ECG findings in QT interval

Secondary Endpoints
Safety and tolerability: Viral shedding analysis
1 year
Assessment of Immunogenicity: Biomarkers in serum
1 year
Assessment of Immunogenicity: Biomarkers in peripheral blood mononuclear cells (PBMCs
5 years
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Study Design & Arms
AllocationNA
MaskingNONE
ModelSINGLE_GROUP
PurposeTREATMENT
Treatment Arms
ArmTypeDescription
TSHA-101EXPERIMENTALSubjects who will receive one-time intrathecal TSHA-101, brain volume based sliding scale for dosage
Interventions
NameTypeDescription
TSHA-101BIOLOGICALAAV9 viral vector containing HEXA and HEXB genes to be administered via Intrathecal injection
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Eligibility Criteria
Age RangeN/A to 15 Months
SexALL
Healthy VolunteersNo
Study Sites1

Key Inclusion Criteria: * male or female with age less than or equal to 15 months * diagnosis of GM2 gangliosidosis with genetic and enzymatic documentation of infantile disease Key Exclusion Criteria: * a second neurodevelopmental disorder independent of the HEXA or HEXB * inability to tolerate ...

Countries:Canada
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Recent Changes (Last 90 Days)
LOWMay 26, 2026NCT04798235primaryCompletionDate: changed
LOWMay 24, 2026NCT04798235studyFirstPostDate: changed