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rhASA- Dose Level 1

Phase 1

Metachromatic Leukodystrophy (MLD) | Monoclonal antibody | Rare Disease |Takeda Pharmaceutical Company Limited|Last Updated: Jun 25, 2021

Success Probability

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Market & Valuation

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Trial Design

CONTROLLEDDMC
Total Trials1
Total Enrollment13

FDA Designations

No designations recorded

Clinical trial landscape

rhASA- Dose Level 1 · 1 trial · 1 indication

Phase 1 1
NCT00418561Metazym for the Treatment of Patients With Late Infantile Metachromatic Leukodystrophy (MLD)Metachromatic Leukodystrophy (MLD)
COMPLETED13 Analytics
PHASE1COMPLETED
Metazym for the Treatment of Patients With Late Infantile Metachromatic Leukodystrophy (MLD)
Metachromatic Leukodystrophy (MLD)Unlock trial analytics

Study Endpoints

Primary Endpoints

Number of Participants With Treatment-emergent Adverse Events (TEAEs)
From study drug administration up to Week 28

An adverse event (AE) is any untoward, undesired, unplanned clinical event in the form of signs, symptoms, disease, or laboratory or physiological observations occurring in a participant, participating in a clinical study with study drug, regardless of causal relationship. TEAEs were AEs occurred after study drug administration that were absent before treatment or that worsened relative to pre-treatment state, up to Week 28 until evaluation (when last cohort had 26-week evaluation and data management performed within 4 weeks) completed.

Change From Baseline in Gross Motor Function Measure (GMFM) at Week 26
Baseline, Week 26

GMFM was measured using GMFM-88 item scores and summed to calculate a total GMFM-88 score. For each GMFM-88 item, the score was between 0 (minimal) to 3 (maximum). The total GMFM-88 score was between 0 (minimal) and 264 (maximum). The decrease in GMFM score over time indicates worsening of disease over time. Relative change from baseline at Week 26 was calculated as percentage change from baseline divided by the age-difference in months between first and last visit. Adjusted mean and 95 percent (%) confidence intervals were reported.

Change From Baseline in Cerebrospinal Fluid (CSF) Sulfatide at Week 26
Baseline, Week 26

Relative change from baseline at Week 26 was calculated as percentage change from baseline divided by the age-difference in months between first and last visit. Adjusted mean and 95 percent (%) confidence intervals were reported.

Number of Participants With Shift From Baseline to Week 26 in Sulfatide Levels in Urine
Baseline up to Week 26

Number of participants with shifts between negative (value=0) and positive (value=1) values in urine sulfatide levels from baseline at Week 26 is reported.

Change From Baseline in Mullen's Scales of Early Learning at Week 26
Baseline, Week 26

Mullen's Scales of Early Learning is used to assess performance and learning ability in young children. The scale consisted of 144 items that had specific scoring criteria for each item. The scores were converted to T-scores with a decrease in score indicating worsening of disease. Relative change from baseline at Week 26 was calculated as percentage change from baseline divided by the age-difference in months between first and last visit. Adjusted mean and 95 percent (%) confidence intervals were reported.

Maximum Plasma Drug Concentration (Cmax) of Recombinant Human Arylsulphatase A (rhASA)
Pre-dose and post-dose at 20, 40, 90 minutes, 3, 6 and 8 hours on Day 0, 40 minutes post-dose at Week 4, Pre-dose and post-dose at 20, 40, 90 minutes, 3, 6 and 8 hours at Week 8
Arylsulfatase A (ASA) Activity in Leukocytes
Pre-dose and post-dose at 24 hours on Day 0 and at Weeks 8 and 26

Secondary Endpoints

Change From Baseline in Nerve Conduction Velocity at Week 26
Baseline, Week 26
Number of Participants Who Had Undergone Nerve Biopsy and Had a Normal Nerve at Both Baseline and Week 26
Baseline, Week 26
Number of Participants With Shift From Baseline to Week 26 in Magnetic Resonance Imaging (MRI)-Loes Scores
Baseline up to Week 26
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Study Design & Arms

AllocationNON_RANDOMIZED
MaskingNONE
ModelFACTORIAL
PurposeTREATMENT

Treatment Arms

ArmTypeDescription
Cohort 1EXPERIMENTALMetazym (Recombinant human arylsulfatase A (rhASA)): 25 U/kg as a single dose - hereafter 50 U/kg
Cohort 2EXPERIMENTAL100 U/kg Metazym (Recombinant human arylsulfatase A (rhASA))
Cohort 3EXPERIMENTAL200 U/kg Metazym (Recombinant human arylsulfatase A (rhASA))

Interventions

NameTypeDescription
rhASA - Dose Level 1BIOLOGICALIntravenous infusion 25 U/kg as a single dose - hereafter 50 U/kg every other week for 26 weeks
rhASA - Dose Level 2BIOLOGICALIntravenous infusion 100 U/kg every other week for 26 weeks
rhASA - Dose Level 3BIOLOGICALIntravenous infusion 200 U/kg every other week for 26 weeks
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Eligibility Criteria

Age Range1 Year to 5 Years
SexALL
Healthy VolunteersNo
Study Sites1

Inclusion Criteria: 1. Subject's legally authorized guardian(s) must provide signed, informed consent prior to performing any study-related activities (Trial-related activities are any procedures that would not have been performed during normal management of the subject). 2. The patient must have a...

Countries:Denmark
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Frequently asked questions about rhASA- Dose Level 1

What is rhASA- Dose Level 1 used for?

rhASA- Dose Level 1 is an investigational therapy being studied for the treatment of Metachromatic Leukodystrophy (MLD), a rare genetic disorder. It is currently in Phase 1 clinical development and has not been approved by regulatory authorities.

Who makes rhASA- Dose Level 1?

rhASA- Dose Level 1 is being developed by Takeda Pharmaceutical Company Limited, which trades under the ticker TAK. The company is conducting clinical research on this investigational therapy for Metachromatic Leukodystrophy.

What phase is rhASA- Dose Level 1 in?

rhASA- Dose Level 1 is in Phase 1 clinical development. It is an investigational therapy and has not been approved for commercial use. The Phase 1 trial has been completed, and the drug remains under clinical investigation.

What clinical trials is rhASA- Dose Level 1 in?

rhASA- Dose Level 1 was studied in a completed Phase 1 clinical trial with the identifier NCT00418561. The trial, titled 'Metazym for the Treatment of Patients With Late Infantile Metachromatic Leukodystrophy (MLD),' enrolled 13 participants in Denmark.

Is rhASA- Dose Level 1 the same as Metazym?

rhASA- Dose Level 1 is associated with the trial name Metazym, as indicated in the clinical trial title. The investigational therapy is being studied for Metachromatic Leukodystrophy, and the trial was conducted in Denmark.