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SHP611

Phase 2

Metachromatic Leukodystrophy (MLD) | Small molecule | Rare Disease |Takeda Pharmaceutical Company Limited|Last Updated: Jul 10, 2026

Success Probability

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Market & Valuation

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Trial Design

UNCONTROLLEDDMC
Total Trials1
Total Enrollment36

FDA Designations

No designations recorded

Clinical trial landscape

SHP611 · 1 trial · 1 indication

Phase 2 1
NCT03771898A Study of Intrathecal SHP611 in Children With Metachromatic LeukodystrophyMetachromatic Leukodystrophy (MLD)
COMPLETED36 Analytics
PHASE2COMPLETED
A Study of Intrathecal SHP611 in Children With Metachromatic Leukodystrophy
Metachromatic Leukodystrophy (MLD)Unlock trial analytics

Study Endpoints

Primary Endpoints

Percent Probability of Free of Loss of Locomotion in the Last Time Interval Up to 2 Years (Week 106) Based on GMFC-MLD for SHP611 Group A and GLIA-MLD Matched External Control
Baseline up to Week 106

Loss of locomotion was estimated using interval censoring survival analysis. Survival probability free of loss of locomotion based on GMFC-MLD was estimated up to Week 106 (or two years), with associated 2-sided 95 percent (%) confidence interval (CI). GMFC-MLD scale consists of 7 categories, scores ranging from 0 (walking without support with quality of performance normal for age) to 6 (loss of any locomotion as well as loss of any head and trunk control). Higher scores mean a worse outcome. The data was reported in terms of Mean as survival function was quantified using a weighted average of percentage of participants not reaching the event of interest, with weights derived from the relative size of treated and control units in the strata used for the stratified log-rank test in the primary analysis.

Secondary Endpoints

Group A: Number of Participants Who Maintained Their Gross Motor Function Evaluated by Using the GMFC-MLD at Week 106 Compared With Matched External Control Group Data
Baseline up to Week 106
Number of Participants With Change From Baseline in Gross Motor Function Evaluated by Using the GMFC-MLD at Week 106
Baseline, Week 106
Group A: Number of Participants With Decline From Baseline in GMFC-LMD of More Than 2 Categories
Baseline, Week 106
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Study Design & Arms

AllocationNA
MaskingNONE
ModelSINGLE_GROUP
PurposeTREATMENT

Treatment Arms

ArmTypeDescription
SHP611EXPERIMENTALParticipants will receive 150 milligrams (mg) of SHP611 intrathecally (IT) via intrathecal drug delivery device (IDDD) or lumbar puncture (LP) once weekly for 106 weeks in six groups (Group A, B, C, D, E, and F) based on participant's age and motor dysfunction.

Interventions

NameTypeDescription
SHP611DRUGParticipants will receive 150 mg of SHP611 IT via IDDD or LP once weekly for 106 weeks.
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Eligibility Criteria

Age Range6 Months to 72 Months
SexALL
Healthy VolunteersNo
Study Sites30

Inclusion Criteria: * The participant must have a documented diagnosis of MLD (Groups A-F): 1. Low ASA activity in leukocytes (compared to laboratory normal range). 2. Elevated sulfatides in urine. * The participant must have a gait disorder due to spastic ataxia or weakness attributable to ML...

Countries:United StatesArgentinaBelgiumBrazilCanadaFranceGermanyGreeceIsraelItalyJapanNetherlandsSpainUnited Kingdom
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Recent Changes (Last 90 Days)

MEDIUMAug 10, 2026NCT03771898TRIAL_REMOVED: changed
MEDIUMAug 10, 2026NCT03771898TRIAL_REMOVED: changed
HIGHJul 10, 2026NCT03771898Status: ACTIVE_NOT_RECRUITING → COMPLETED
HIGHJul 10, 2026NCT03771898Status: ACTIVE_NOT_RECRUITING → COMPLETED

Frequently asked questions about SHP611

What is SHP611 used for?

SHP611 is an investigational small molecule being studied for the treatment of Metachromatic Leukodystrophy (MLD), a rare genetic disorder. It is administered intrathecally and is currently in clinical development, though it is not approved by regulatory authorities.

Who makes SHP611?

SHP611 is being developed by Takeda Pharmaceutical Company Limited, a global biopharmaceutical company listed on the stock exchange under the ticker symbol TAK. The drug is in Phase 2 clinical development for Metachromatic Leukodystrophy.

What phase is SHP611 in?

SHP611 is in Phase 2 clinical development. A Phase 2 study of intrathecal SHP611 in children with Metachromatic Leukodystrophy has been completed. The drug remains investigational and has not received regulatory approval.

What clinical trials is SHP611 in?

SHP611 has been studied in one clinical trial, identified as NCT03771898, titled "A Study of Intrathecal SHP611 in Children With Metachromatic Leukodystrophy." This Phase 2 study enrolled 36 participants and has been completed. The trial was conducted across multiple countries including the United States, Argentina, Belgium, Brazil, Canada, France, Germany, Greece, Israel, Italy, Japan, Netherlands, Spain, and the United Kingdom.

Is SHP611 FDA approved?

SHP611 is not FDA approved. It is an investigational drug currently in Phase 2 clinical development for Metachromatic Leukodystrophy. The completed Phase 2 trial, NCT03771898, evaluated the drug in children, but regulatory approval has not been granted.