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STK-001- Single Ascending Doses

Phase 1

Dravet Syndrome | Small molecule | Neurology |Stoke Therapeutics, Inc.|Last Updated: May 18, 2025

Success Probability

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Market & Valuation

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Trial Design

CONTROLLEDDMC
Total Trials1
Total Enrollment62

FDA Designations

No designations recorded

Clinical trial landscape

STK-001- Single Ascending Doses · 1 trial · 1 indication

Phase 1 1
NCT04442295An Open-Label Study to Investigate the Safety of Single and Multiple Ascending Doses in Children and Adolescents With Dravet SyndromeDravet Syndrome
COMPLETED62 Analytics
PHASE1COMPLETED
An Open-Label Study to Investigate the Safety of Single and Multiple Ascending Doses in Children and Adolescents With Dravet Syndrome
Dravet SyndromeUnlock trial analytics

Study Endpoints

Primary Endpoints

Safety and Tolerability of single and multiple doses of STK-001 with respect to:
Screening (Day -28) until 6 months after single and multiple drug dosing

1. Incidence of adverse events 2. incidence of abnormal vital signs 3. Abnormal physical examination findings 4. Abnormal 12-lead electrocardiogram (ECG) 5. Abnormal laboratory parameters

Pharmacokinetic (PK) Parameters
Day 1 (Dosing) until 6 months after single and multiple drug dosing

Analysis of plasma concentrations of STK-001

Exposure of STK-001 in Cerebrospinal Fluid (CSF)
Day 1 (Dosing) until 6 months after single and multiple drug dosing

Measurement of STK-001 concentrations

Secondary Endpoints

Measurement of seizure frequency
Screening (Day -28) until 6 months after single and multiple drug dosing
Change in Caregiver Global Impression of Change Scale
Baseline (Day -1) until 6 months after single and multiple drug dosing
Change in Clinician-assessed Global Impression of Change Scale
Baseline (Day -1) until 6 months after single and multiple drug dosing
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Study Design & Arms

AllocationNON_RANDOMIZED
MaskingNONE
ModelSEQUENTIAL
PurposeTREATMENT

Treatment Arms

ArmTypeDescription
Single Ascending DosesEXPERIMENTALEnrollment of patients in two age groups. A Sentinel group of 2 patients aged 13 to 18 years of age, inclusive, and an expanded group of 2 patients 2 to 12 years of age to receive single doses. There will be an option to dose up to 6 additional patients at each dose level and an option to expand the maximum tolerated dose level with 5 additional patients.
Multiple Ascending DosesEXPERIMENTALEnrollment of patients in two age groups. A Sentinel group of 2 patients aged 13 to 18 years of age, inclusive, and an expanded group of 2 patients 2 to 12 years of age to receive multiple doses. There will be an option to dose up to 6 additional patients at each dose level and an option to expand the maximum tolerated dose level with 10 additional patients.

Interventions

NameTypeDescription
STK-001 - Single Ascending DosesDRUGExperimental : Single Ascending Doses - STK-001 drug product is an antisense oligonucleotide administered as an intrathecal injection. Four dose levels will be evaluated ( 10mg, 20mg,30mg, 45mg and 70mg ).
STK-001 - Multiple Ascending DosesDRUGExperimental : Multiple Ascending Doses - STK-001 drug product is an antisense oligonucleotide administered as an intrathecal injection. Three dose levels will be evaluated ( 20mg,30mg and 45mg ).
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Eligibility Criteria

Age Range2 Years to 18 Years
SexALL
Healthy VolunteersNo
Study Sites18

Inclusion Criteria: * Diagnosis of Dravet Syndrome (DS) with onset of recurrent focal motor or hemiconvulsive or generalized tonic-clonic seizures prior to 12 months of age, which are often prolonged and triggered by hyperthermia. * No history of causal MRI lesion * No other known etiology *...

Countries:United States
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Frequently asked questions about STK-001- Single Ascending Doses

What is STK-001 used for in Dravet Syndrome?

STK-001 is an investigational small molecule being studied for the treatment of Dravet Syndrome, a severe form of childhood epilepsy. It is currently in Phase 1 clinical development and is not yet approved by regulatory authorities. The drug is designed to address the underlying genetic cause of the condition, though its exact mechanism is not specified.

Who makes STK-001?

STK-001 is being developed by Stoke Therapeutics, Inc., a biopharmaceutical company listed on the NASDAQ under the ticker symbol STOK. The company is conducting clinical trials to evaluate the safety and tolerability of STK-001 in pediatric patients with Dravet Syndrome.

What phase is STK-001 in?

STK-001 is currently in Phase 1 clinical development. A Phase 1 study has been completed, which evaluated the safety of single and multiple ascending doses in children and adolescents with Dravet Syndrome. The drug remains investigational and has not received FDA approval.

What clinical trials is STK-001 in?

STK-001 has one completed clinical trial registered under NCT04442295, titled "An Open-Label Study to Investigate the Safety of Single and Multiple Ascending Doses in Children and Adolescents With Dravet Syndrome." This Phase 1 study enrolled 62 participants in the United States and included children as young as 2 years old.

Is STK-001 the same as STK-001- Single Ascending Doses?

Yes, STK-001 is the same drug as STK-001- Single Ascending Doses. The latter name refers to the specific dosing regimen evaluated in the clinical trial. The drug is being developed by Stoke Therapeutics for the treatment of Dravet Syndrome.