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AOC 1020

Phase 2

FSHD | Small molecule | Neurology |Atrium Therapeutics, Inc.|Last Updated: May 14, 2026

Success Probability
Approval Probability 71%
TA Base Rate26%
Adjusted LOA41%
ML RiskLOW_RISK
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Market & Valuation
rNPV $3.2B
Market Size $9.4B
Revenue Basis $1.6B
Competitors 6
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Trial Design
RandomizedDouble-BlindPLACEBO_CONTROLLEDDMCBiomarker
Total Trials2
Total Enrollment174
FDA Designations
No designations recorded
Clinical Trials (2)
NCT IDTitlePhaseStatusEnrollmentVelocityDesignStartCompletionLast UpdatedSitesCountries
NCT06547216Phase 2 Open-label Extension Study of AOC 1020 in Participants With Facioscapulohumeral Muscular Dystrophy (FSHD)PHASE2 ACTIVE NOT_RECRUITING 84Jul 25, 2024Jun 1, 2030May 14, 202617 United States, Canada +1
NCT05747924Phase 1/2 Study of AOC 1020 in Participants With Facioscapulohumeral Muscular Dystrophy (FSHD)PHASE1 COMPLETED 90Apr 4, 2023Mar 20, 2026Apr 24, 202617 United States, Canada +1
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Study Endpoints
Primary Endpoints
Incidence of treatment-emergent adverse events
Through study completion, up to Day 729
Incidence of treatment-emergent adverse events (Cohorts A & B)
Through study completion, up to Day 365
Change in plasma KHDC1L (Part C)
Across months 3 to 12

Ratio to Baseline

Secondary Endpoints
Plasma pharmacokinetic (PK) parameters of AOC 1020 (Cohorts A & B)
Through study completion; up to Day 365
Muscle drug concentration (Cohorts A & B)
Day 120
Change in circulating creatine kinase (Cohort C)
Across months 3 to 12
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Study Design & Arms
AllocationNA
MaskingNONE
ModelSINGLE_GROUP
PurposeTREATMENT
Treatment Arms
ArmTypeDescription
AOC 1020 RegimenEXPERIMENTALAOC 1020 Dose Regimen; Thirty-two doses administered intravenously over 46 months. All participants will receive AOC 1020 at a dose level of 2mg/kg.
AOC 1020 Regimen 1EXPERIMENTALCohort A: AOC 1020 Dose Regimen 1; Five doses administered intravenously over 9 months
AOC 1020 Regimen 2EXPERIMENTALCohort B1: AOC 1020 Dose Regimen 2; Five doses administered intravenously over 9 months
AOC 1020 Regimen 3EXPERIMENTALCohort C: AOC 1020 Dose Regimen 3; Eight doses administered intravenously over approximately 10 months
Placebo (Saline) Regimen 1PLACEBO_COMPARATORCohort A \& B: Placebo; Five doses administered intravenously over 9 months
Placebo (Saline) Regimen 2PLACEBO_COMPARATORCohort C: Placebo; Eight doses administered intravenously over approximately 10 months
Interventions
NameTypeDescription
AOC 1020DRUGAOC 1020 will be administered via intravenous (IV) infusion
PlaceboDRUGPlacebo will be administered via intravenous (IV) infusion
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Eligibility Criteria
Age Range16 Years — 72 Years
SexALL
Healthy VolunteersNo
Study Sites17

Inclusion Criteria: 1. Ability to provide written informed consent (signed and dated) and any authorizations required by local law and be willing and able to comply with all study requirements. When enrolling participants who are minors, it is necessary to also obtain consent from a legally designa...

Countries:United StatesCanadaUnited Kingdom
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Recent Changes (Last 90 Days)
MEDIUMMay 26, 2026NCT06547216Status: ENROLLING_BY_INVITATION → ACTIVE_NOT_RECRUITING
LOWMay 24, 2026NCT06547216studyFirstPostDate: changed