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voretigene neparvovec-rzyl

Phase 1

Leber Congenital Amaurosis | Monoclonal antibody | Rare Disease |Roche Holding AG|Last Updated: Apr 29, 2025

Target and mechanism

Molecular targetRPE65
Target classExogenous Gene
ModalityMonoclonal antibody

Success Probability

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Market & Valuation

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Trial Design

CONTROLLEDDMC
Total Trials2
Total Enrollment24

FDA Designations

No designations recorded

Clinical trial landscape

voretigene neparvovec-rzyl · 2 trials · 1 indication

Phase 1 2
NCT01208389Phase 1 Follow-on Study of AAV2-hRPE65v2 Vector in Subjects With Leber Congenital Amaurosis (LCA) 2Leber Congenital Amaurosis
ACTIVE NOT_RECRUITING12 Analytics
NCT00516477Safety Study in Subjects With Leber Congenital AmaurosisLeber Congenital Amaurosis
COMPLETED12 Analytics
PHASE1ACTIVE NOT_RECRUITING
Phase 1 Follow-on Study of AAV2-hRPE65v2 Vector in Subjects With Leber Congenital Amaurosis (LCA) 2
Leber Congenital AmaurosisUnlock trial analytics
PHASE1COMPLETED
Safety Study in Subjects With Leber Congenital Amaurosis
Leber Congenital AmaurosisUnlock trial analytics

Study Endpoints

Primary Endpoints

Adverse events as a measure of safety and tolerability
15 years

The primary outcome measures are safety and tolerability. Secondary outcome measure(s) include changes in visual function as measured by subjective, psychophysical tests and by objective, physiologic tests.

The primary outcome measures are safety and tolerability. Secondary outcome measure(s) include changes in visual function as measured by subjective, psychophysical tests and by objective, physiologic tests.
Visual function will be measured at designated intervals from baseline visits through 5 years as stated in the protocol.

Secondary Endpoints

Visual acuity
15 years
Visual field
15 years
Pupillary light response
15 years
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Study Design & Arms

AllocationNA
MaskingNONE
ModelSINGLE_GROUP
PurposeTREATMENT

Treatment Arms

ArmTypeDescription
voretigene neparvovec-rzyl (AAV2-hRPE65v2)EXPERIMENTALAdministration of study agent (AAV2-hRPE65v2) to the previously, uninjected contralateral eye:
dose cohort 1EXPERIMENTAL1.5E10 vector genomes voretigene neparvovec-rzyl in 150 microliters administered subretinally
dose cohort 2EXPERIMENTAL4.8E10 vector genomes voretigene neparvovec-rzyl in 150 microliters administered subretinally
dose cohort 3EXPERIMENTAL1.5E11 vector genomes voretigene neparvovec-rzyl in 300 microliters administered subretinally

Interventions

NameTypeDescription
voretigene neparvovec-rzylBIOLOGICALOne time, subretinal administration of 1.5E11 vg AAV2-hRPE65v2 vector in 300 microliters to the contralateral, previously uninjected eye.
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Eligibility Criteria

Age Range8 Years to N/A
SexALL
Healthy VolunteersNo
Study Sites1

Inclusion Criteria: * Prior participation in Phase 1 study with unilateral, subretinal administration of AAV2-hRPE65v2. * Visual acuity equal to or greater than light perception. * Sufficient viable retinal cells in contralateral, previously uninjected eye, as determined by non-invasive means, such...

Countries:United States
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Frequently asked questions about voretigene neparvovec-rzyl

What is voretigene neparvovec-rzyl used for?

Voretigene neparvovec-rzyl is used for Leber Congenital Amaurosis, a rare inherited retinal disease. It is an investigational gene therapy being studied in clinical trials. The drug is not approved and is still in clinical development.

What does voretigene neparvovec-rzyl target?

Voretigene neparvovec-rzyl is a gene therapy that targets the RPE65 gene, which is mutated in Leber Congenital Amaurosis. It delivers a normal copy of the gene to retinal cells to restore function. The target class is gene therapy.

Who makes voretigene neparvovec-rzyl?

Voretigene neparvovec-rzyl is developed by Roche Holding AG, traded as RHHBY on the OTC market. Roche is the developer of this investigational gene therapy for Leber Congenital Amaurosis.

What phase is voretigene neparvovec-rzyl in?

Voretigene neparvovec-rzyl is in Phase 1 clinical development. It is an investigational drug, not FDA approved. There are two Phase 1 trials, one completed and one active but not recruiting.

What clinical trials is voretigene neparvovec-rzyl in?

Voretigene neparvovec-rzyl has two Phase 1 trials. NCT00516477 is a completed safety study in subjects with Leber Congenital Amaurosis. NCT01208389 is an active, not recruiting follow-on study of the vector in LCA2. Both enrolled 12 participants.

Is voretigene neparvovec-rzyl the same as AAV2-hRPE65v2?

Voretigene neparvovec-rzyl is associated with the vector AAV2-hRPE65v2, as named in the clinical trial titles. The trials study this vector in subjects with Leber Congenital Amaurosis. The drug is also known by this vector name.