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SPK-3006

Phase 1

Pompe Disease | Gene therapy | Rare Disease |Roche Holding AG|Last Updated: Nov 27, 2024

Success Probability

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Market & Valuation

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Trial Design

UNCONTROLLEDDMC
Total Trials1
Total Enrollment4

FDA Designations

No designations recorded

Clinical trial landscape

SPK-3006 · 1 trial · 7 indications

Phase 1 1
NCT04093349A Gene Transfer Study for Late-Onset Pompe Disease (RESOLUTE)Pompe Disease
ACTIVE NOT_RECRUITING4 Analytics
PHASE1ACTIVE NOT_RECRUITING
A Gene Transfer Study for Late-Onset Pompe Disease (RESOLUTE)
Pompe DiseaseUnlock trial analytics

Study Endpoints

Primary Endpoints

Number of adverse and serious adverse events (AEs/SAEs), including clinically significant abnormal laboratory values.
Up to 5 years

Adverse events.

Occurrence of immune response against AAV capsid
Up to 5 years
Occurrence of immune response against GAA transgene
Up to 5 years
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Study Design & Arms

AllocationNA
MaskingNONE
ModelSEQUENTIAL
PurposeTREATMENT

Treatment Arms

ArmTypeDescription
SPK-3006EXPERIMENTALAll participants who meet the eligibility criteria will receive a single intravenous (i.v.) administration of SPK-3006.

Interventions

NameTypeDescription
SPK-3006GENETICadeno-associated viral (AAV) vector
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Eligibility Criteria

Age Range18 Years to N/A
SexALL
Healthy VolunteersNo
Study Sites29

Inclusion Criteria: * Provide written informed consent; * Males and Females ≥18 years of age with late-onset Pompe disease; * Received ERT for at least the previous 24 months * Have clinically moderate, late-onset Pompe disease characteristics; * Agree to use reliable contraception. Exclusion Crit...

Countries:United StatesCanadaDenmarkFranceGermanyItalyNetherlandsUnited Kingdom
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Frequently asked questions about SPK-3006

What is SPK-3006 used for?

SPK-3006 is an investigational gene therapy being developed for the treatment of Pompe disease, a rare lysosomal storage disorder. It is specifically being studied in patients with late-onset Pompe disease, also known as glycogen storage disease type 2 or acid maltase deficiency. The therapy is currently in Phase 1 clinical development.

What does SPK-3006 target?

SPK-3006 is a gene therapy designed to address the underlying genetic cause of Pompe disease. The therapy is intended to deliver a functional gene to produce the enzyme acid alpha-glucosidase, which is deficient in patients with Pompe disease. This enzyme is responsible for breaking down glycogen in cells, and its deficiency leads to the accumulation of glycogen, particularly in muscle tissue.

Who makes SPK-3006?

SPK-3006 is being developed by Roche Holding AG, a multinational healthcare company. Roche's stock is traded on the OTC market under the ticker symbol RHHBY. The company is conducting clinical trials to evaluate the safety and efficacy of SPK-3006 in patients with late-onset Pompe disease.

What phase is SPK-3006 in?

SPK-3006 is currently in Phase 1 clinical development. It is an investigational gene therapy that has not yet been approved by regulatory authorities. The ongoing Phase 1 trial is designed to evaluate the safety, tolerability, and preliminary efficacy of SPK-3006 in patients with late-onset Pompe disease.

What clinical trials is SPK-3006 in?

SPK-3006 is being evaluated in a Phase 1 clinical trial with the identifier NCT04093349, titled "A Gene Transfer Study for Late-Onset Pompe Disease (RESOLUTE)." This trial is currently active but not recruiting participants. The study is enrolling approximately 4 adult patients with late-onset Pompe disease across multiple countries, including the United States, Canada, and several European nations.

Is SPK-3006 the same as other gene therapies for Pompe disease?

SPK-3006 is a specific gene therapy candidate developed by Roche for late-onset Pompe disease. It is distinct from other gene therapies in development for this condition, as each therapy uses different viral vectors and delivery methods. The RESOLUTE trial is evaluating SPK-3006 as a potential one-time treatment to address the root cause of the disease.