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Triheptanoin

Phase 3

Long-chain Fatty Acid Oxidation Disorders (LC-FAOD) | Small molecule | Other |Ultragenyx Pharmaceutical Inc.|Last Updated: Apr 7, 2026

Success Probability
Approval Probability 71%
TA Base Rate26%
Adjusted LOA41%
ML RiskLOW_RISK
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Market & Valuation
rNPV $3.2B
Market Size $9.4B
Revenue Basis $1.6B
Competitors 6
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Trial Design
RandomizedDouble-BlindACTIVE_CONTROLLEDDMCBiomarker
Total Trials1
Total Enrollment69
FDA Designations
No designations recorded
Clinical Trials (1)
NCT IDTitlePhaseStatusEnrollmentVelocityDesignStartCompletionLast UpdatedSitesCountries
NCT05933200A Study to Determine the Effect of Triheptanoin Compared With Even-Chain MCT on MCEs in Pediatric Patients With LC-FAODPHASE3 ACTIVE NOT_RECRUITING 69Feb 28, 2023Aug 1, 2027Apr 7, 202615 Czechia, Germany +5
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Study Endpoints
Primary Endpoints
Annualized Event Rate of Major Clinical Events (MCEs)
Up to Year 4
Secondary Endpoints
Annualized Duration of MCEs
Up to Year 4
Annualized Hypoglycemic Event-rate Captured as MCEs and At-home Clinical Events (HCEs)
Up to Year 4
Clinical Global Impression of Change [CGI-C] Scale Score
Up to Year 4
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Study Design & Arms
AllocationRANDOMIZED
MaskingQUADRUPLE
ModelPARALLEL
PurposeTREATMENT
Treatment Arms
ArmTypeDescription
TriheptanoinEXPERIMENTALParticipants will be given prescriptions for triheptanoin in mL/day, which will be divided into approximately 4 administrations per day, with precise instructions for administration. Triheptanoin will be titrated up to the first 6 weeks of the study. After titration, the dose is to remain stable for the remainder of the Double-blind Treatment Period. Following the Double-blind Treatment Period, open-label triheptanoin will be provided at participants' current dose during an Open Access Period, if no other options to receive trihepatnoin are available locally.
MCTACTIVE_COMPARATORParticipants will be given prescriptions for MCT in mL/day, which will be divided into approximately 4 administrations per day, with precise instructions for administration. MCT will be titrated up to the first 6 weeks of the study. After titration, the dose is to remain stable for the remainder of the Double-blind Treatment Period. Following the Double-blind Treatment Period, open-label triheptanoin will be provided at participants' current dose during an Open Access Period, if no other options to receive trihepatnoin are available locally.
Interventions
NameTypeDescription
TriheptanoinDRUGLiquid for oral (PO) or enteral feeding tube administration
MCT OilDIETARY_SUPPLEMENTLiquid for oral (PO) or enteral feeding tube administration
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Eligibility Criteria
Age RangeN/A — 17 Years
SexALL
Healthy VolunteersNo
Study Sites15

Inclusion Criteria for Main Study: * Males and females, from 0 (including newborns) to \< 18 years of age at time of randomization * Confirmed diagnosis of LC-FAOD * Have a caregiver(s) willing and able to assist in all applicable study requirements * Have a legally authorized representative willin...

Countries:CzechiaGermanyJapanPolandSaudi ArabiaSpainTurkey (Türkiye)
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Recent Changes (Last 90 Days)
LOWMay 26, 2026NCT05933200primaryCompletionDate: changed
LOWMay 24, 2026NCT05933200studyFirstPostDate: changed