Recent Updates
Recently added Catalysts

sepofarsen

Phase 2

Leber Congenital Amaurosis 10 | Small molecule | Rare Disease |ProQR Therapeutics N.V.|Last Updated: Mar 17, 2022

Success Probability
Approval Probability 71%
TA Base Rate26%
Adjusted LOA41%
ML RiskLOW_RISK
Premium
Market & Valuation
rNPV $3.2B
Market Size $9.4B
Revenue Basis $1.6B
Competitors 6
Premium
Trial Design
RandomizedDouble-BlindACTIVE_CONTROLLEDDMCBiomarker
Total Trials1
Total Enrollment36
FDA Designations
No designations recorded
Clinical Trials (1)
NCT IDTitlePhaseStatusEnrollmentVelocityDesignStartCompletionLast UpdatedSitesCountries
NCT03913143A Study to Evaluate Efficacy, Safety, Tolerability and Exposure After a Repeat-dose of Sepofarsen (QR-110) in LCA10 (ILLUMINATE)PHASE2 ACTIVE NOT_RECRUITING 36Apr 4, 2019Mar 1, 2023Mar 17, 202214 United States, Belgium +7
Unlock Drug Trial Details
Study Endpoints
Primary Endpoints
Change in BCVA
12 months

Change in Best-corrected visual acuity (BCVA) relative to baseline after 12 months of treatment versus sham-procedure

Secondary Endpoints
Change from baseline in BCVA ≤ -0.3 LogMAR
12 and 24 months
Clinical meaningful improvement in subjects with BCVA ≤ 1.7 LogMAR
12 and 24 months
Change in BCVA based on FrACT
12 and 24 months
Unlock Study Endpoints
Study Design & Arms
AllocationRANDOMIZED
MaskingQUADRUPLE
ModelPARALLEL
PurposeTREATMENT
Treatment Arms
ArmTypeDescription
Group 1: Dose 1 sepofarsen (QR-110)EXPERIMENTALInitial loading dose, followed by maintenance doses at month 3 and every 6 months there after, administered by intravitreal injection (24 months duration of treatment). After 12 months treatment of the contralateral eye may be initiated
Group 2: Dose 2 sepofarsen (QR-110)ACTIVE_COMPARATORInitial loading dose, followed by maintenance doses at month 3 and every 6 months there after, administered by intravitreal injection (24 months duration of treatment). After 12 months treatment of the contralateral eye may be initiated
Group 3: ShamSHAM_COMPARATORSham procedure (no experimental drug administered), Day 1, month 3 and every six months there after. After 12 months cross over to active study drug may be initiated
Interventions
NameTypeDescription
sepofarsenDRUGRNA antisense oligonucleotide for intravitreal injection
ShamOTHERSham-Procedure (no experimental drug administered)
Unlock Study Design Details
Eligibility Criteria
Age Range8 Years — N/A
SexALL
Healthy VolunteersNo
Study Sites14

Main Inclusion Criteria Relating to Study Initiation: * Male or female, ≥ 8 years of age at Screening with a clinical diagnosis of LCA10 and a molecular diagnosis of homozygosity or compound heterozygosity for the c.2991+1655A\>G mutation, based on genotyping analysis at Screening. A historic genot...

Countries:United StatesBelgiumBrazilCanadaFranceGermanyItalyNetherlandsUnited Kingdom
Unlock Eligibility Criteria
Recent Changes (Last 90 Days)
LOWMay 26, 2026NCT03913143primaryCompletionDate: changed
LOWMay 24, 2026NCT03913143studyFirstPostDate: changed