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PGN-EDODM1

Phase 2

Myotonic Dystrophy 1 | Small molecule | Rare Disease |PepGen Inc.|Last Updated: Jul 29, 2026

Target and mechanism

Molecular targetDMPK CUG repeat expansion
ModalitySmall molecule

Success Probability

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Market & Valuation

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Trial Design

RandomizedDouble-BlindPLACEBO_CONTROLLEDDMC
Total Trials2
Total Enrollment72

FDA Designations

ORPHAN_DRUGFAST_TRACKRARE_PEDIATRIC_DISEASE

Clinical trial landscape

PGN-EDODM1 · 2 trials · 1 indication

Phase 2 2
NCT07220603An Open-Label Extension Study of PGN-EDODM1 in People With Myotonic Dystrophy Type 1 (FREEDOM-OLE)Myotonic Dystrophy 1
RECRUITING48 Analytics
NCT06667453A Clinical Study of PGN-EDODM1 in People With Myotonic Dystrophy Type 1Myotonic Dystrophy 1
RECRUITING24 Analytics
PHASE2RECRUITING
An Open-Label Extension Study of PGN-EDODM1 in People With Myotonic Dystrophy Type 1 (FREEDOM-OLE)
Myotonic Dystrophy 1Unlock trial analytics
PHASE2RECRUITING
A Clinical Study of PGN-EDODM1 in People With Myotonic Dystrophy Type 1
Myotonic Dystrophy 1Unlock trial analytics

Study Endpoints

Primary Endpoints

Safety and tolerability as assessed by number of participants with Adverse Events (AEs)
Baseline through Week 108

Secondary Endpoints

Maximum Observed Plasma Drug Concentration (Cmax) of PGN-EDODM1
Day 1 through Day 84
Time to Maximum Observed Plasma Drug Concentration (Tmax) of PGN-EDODM1
Day 1 through Day 84
Apparent Terminal Half-Life (t½) of PGN-EDODM1
Day 1 through Day 84
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Study Design & Arms

AllocationNA
MaskingNONE
ModelSINGLE_GROUP
PurposeTREATMENT

Treatment Arms

ArmTypeDescription
PGN-EDODM1EXPERIMENTALParticipants will receive doses of PGN-EDODM1 once every 4 weeks (Q4W)
PlaceboPLACEBO_COMPARATORParticipants randomized to the placebo arm will receive doses of saline (0.9% NaCl), once every 4 weeks (Q4W) for 12 weeks

Interventions

NameTypeDescription
PGN-EDODM1DRUGAdministered by intravenous (IV) infusion
PlaceboOTHERAdministered by intravenous (IV) infusion
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Eligibility Criteria

Age Range16 Years to 65 Years
SexALL
Healthy VolunteersNo
Study Sites3

Inclusion Criteria: * Participant has completed a prior study with PGN-EDODM1 Exclusion Criteria: * Abnormal laboratory tests at screening considered clinically significant by the Investigator * Use of an investigational drug (other than PGN-EDODM1), device, or product, within 30 days or 5 half-l...

Countries:CanadaNew ZealandSouth KoreaUnited Kingdom
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Recent Changes (Last 90 Days)

LOWJul 29, 2026NCT06667453lastUpdatePostDate: changed
LOWJul 29, 2026NCT06667453lastUpdatePostDate: changed

Frequently asked questions about PGN-EDODM1

What is PGN-EDODM1 used for in Myotonic Dystrophy 1?

PGN-EDODM1 is an investigational small molecule being developed for the treatment of Myotonic Dystrophy Type 1 (DM1). It is currently in Phase 2 clinical development and has not been approved by regulatory authorities. The drug is being studied in patients with DM1 to evaluate its safety and efficacy.

What does PGN-EDODM1 target?

PGN-EDODM1 targets the DMPK CUG repeat expansion, which is the underlying genetic cause of Myotonic Dystrophy Type 1. By targeting this specific molecular abnormality, the drug aims to address the root cause of the disease rather than just managing symptoms.

Who is developing PGN-EDODM1?

PGN-EDODM1 is being developed by PepGen Inc., a biopharmaceutical company publicly traded under the ticker symbol PEPG. The company is conducting clinical trials to evaluate the drug's potential as a treatment for Myotonic Dystrophy Type 1.

What phase is PGN-EDODM1 in?

PGN-EDODM1 is currently in Phase 2 clinical development. It is an investigational drug and has not received regulatory approval. The drug has been granted Orphan Drug, Fast Track, and Rare Pediatric Disease designations by the FDA for the treatment of Myotonic Dystrophy Type 1.

What clinical trials is PGN-EDODM1 in?

PGN-EDODM1 is being evaluated in two Phase 2 clinical trials. NCT06667453 is a randomized, double-blind, placebo-controlled study enrolling 24 participants in Canada, New Zealand, South Korea, and the United Kingdom. NCT07220603 is an open-label extension study enrolling 48 participants in Canada. Both trials are currently recruiting.

Is PGN-EDODM1 the same as FREEDOM?

PGN-EDODM1 is not the same as FREEDOM. FREEDOM refers to the clinical trial program for PGN-EDODM1. Specifically, NCT07220603 is titled 'An Open-Label Extension Study of PGN-EDODM1 in People With Myotonic Dystrophy Type 1 (FREEDOM-OLE)', indicating that FREEDOM is the name of the study, not an alternative name for the drug itself.