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DFT383

Phase 1

Nephropathic Cystinosis | Gene therapy | Other |Novartis AG|Last Updated: May 29, 2026

Success Probability
Approval Probability 71%
TA Base Rate26%
Adjusted LOA41%
ML RiskLOW_RISK
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Market & Valuation
rNPV $3.2B
Market Size $9.4B
Revenue Basis $1.6B
Competitors 6
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Trial Design
NO_TREATMENT_CONTROLLEDDMCBiomarker
Total Trials1
Total Enrollment30
FDA Designations
No designations recorded
Clinical Trials (1)
NCT IDTitlePhaseStatusEnrollmentVelocityDesignStartCompletionLast UpdatedSitesCountries
NCT06910813DFT383 in Pediatric Participants With Nephropathic CystinosisPHASE1 RECRUITING 30Jun 2, 2025Mar 14, 2044May 29, 20264 United States
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Study Endpoints
Primary Endpoints
Core Phase - Incidence of adverse events (Cohort 1)
Up to 32 months

Number and proportion of participants with adverse events (AEs) and serious adverse events (SAEs)

Core Phase - Number of participants with hematological reconstitution (Cohort 1)
42 days post DFT infusion

Hematological reconstitution by Day 42 post-DFT383 infusion

Core Phase - Proportion of participants with reversal of renal Fanconi syndrome (RFS)
Up to 32 months

Proportion of participants with reversal of renal Fanconi syndrome (RFS)

Secondary Endpoints
Core Phase - Number of participants independent from cysteamine
up to 24 months
Core Phase - Health-related quality of life (HRQOL)
Up to 32 months
Core Phase - Time from infusion to reversal of RFS (Cohort 1)
Up to 24 months
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Study Design & Arms
AllocationNON_RANDOMIZED
MaskingNONE
ModelPARALLEL
PurposeTREATMENT
Treatment Arms
ArmTypeDescription
Cohort 1 (DFT383)EXPERIMENTALTreatment with DFT383
Cohort 0 (SoC)NO_INTERVENTIONNo study treatment, will continue with standard of care (cysteamine).
Interventions
NameTypeDescription
DFT383GENETICDFT383 is an autologous hematopoietic stem cell (HSC) gene therapy.
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Eligibility Criteria
Age Range2 Years — 5 Years
SexALL
Healthy VolunteersNo
Study Sites4

Key Inclusion Criteria: Participants eligible for inclusion in this study must meet all the following criteria: 1. Informed consent in writing from parent(s) or legal guardian(s) must be provided 2. 2 to 5 years of age (including 5 years and 364 days old) at Screening 3. Weight-for-stature is ≥ th...

Countries:United States
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Recent Changes (Last 90 Days)
LOWMay 29, 2026NCT06910813lastUpdatePostDate: changed
LOWMay 29, 2026NCT06910813lastUpdatePostDate: changed
LOWMay 29, 2026NCT06910813lastUpdatePostDate: changed
LOWMay 26, 2026NCT06910813primaryCompletionDate: changed
LOWMay 24, 2026NCT06910813studyFirstPostDate: changed