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nexiguran ziclumeran

Phase 3

Neuromuscular Disease | Monoclonal antibody | Rare Disease |Intellia Therapeutics, Inc.|Last Updated: Apr 16, 2026

Success Probability
Approval Probability 71%
TA Base Rate26%
Adjusted LOA41%
ML RiskLOW_RISK
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Market & Valuation
rNPV $3.2B
Market Size $9.4B
Revenue Basis $1.6B
Competitors 6
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Trial Design
RandomizedDouble-BlindPLACEBO_CONTROLLEDDMCBiomarker
Total Trials1
Total Enrollment60
FDA Designations
No designations recorded
Clinical Trials (1)
NCT IDTitlePhaseStatusEnrollmentVelocityDesignStartCompletionLast UpdatedSitesCountries
NCT06672237A Phase 3 Study of NTLA-2001 in ATTRv-PNPHASE3 RECRUITING 60Nov 22, 2024Aug 1, 2028Apr 16, 202614 Argentina, Brazil +4
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Study Endpoints
Primary Endpoints
Modified Neuropathy Impairment Score +7 (mNIS+7)
18 Months
Serum TTR
29 Days
Secondary Endpoints
Norfolk Quality of Life-Diabetic Neuropathy (Norfolk QoL-DN) Questionnaire
18 Months
Modified Body Mass Index (mBMI)
18 Months
Serum TTR
18 Months
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Study Design & Arms
AllocationRANDOMIZED
MaskingQUADRUPLE
ModelPARALLEL
PurposeTREATMENT
Treatment Arms
ArmTypeDescription
nexiguran ziclumeranEXPERIMENTALnexiguran ziclumeran 55 mg by single IV infusion
Normal SalinePLACEBO_COMPARATORPlacebo; Normal saline (0.9% NaCl) by single IV infusion
Interventions
NameTypeDescription
nexiguran ziclumeranBIOLOGICALnexiguran ziclumeran 55 mg by single IV infusion
Normal Saline as PlaceboDRUGNormal saline (0.9% NaCl) by single IV infusion
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Eligibility Criteria
Age Range18 Years — 85 Years
SexALL
Healthy VolunteersNo
Study Sites14

Inclusion Criteria: * Diagnosis of ATTRv-PN * Karnofsky Performance Status (KPS) ≥ 60 Exclusion Criteria: * Other causes of amyloidosis (amyloidosis caused by non-TTR protein) * Other known causes of sensorimotor or autonomic neuropathy * Diabetes mellitus * New York Heart Association Class III o...

Countries:ArgentinaBrazilMexicoSingaporeTaiwanThailand
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Recent Changes (Last 90 Days)
LOWMay 26, 2026NCT06672237Status: ACTIVE_NOT_RECRUITING → RECRUITING
LOWMay 24, 2026NCT06672237studyFirstPostDate: changed