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Nomlabofusp

Phase 3

Friedreich Ataxia | Small molecule | Rare Disease |Larimar Therapeutics, Inc.|Last Updated: Aug 31, 2026

Success Probability

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Market & Valuation

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Trial Design

RandomizedDouble-BlindPLACEBO_CONTROLLEDDMC
Total Trials1
Total Enrollment150

FDA Designations

BREAKTHROUGH_THERAPYACCELERATED_APPROVALORPHAN_DRUGRARE_PEDIATRIC_DISEASEFAST_TRACK

Clinical trial landscape

Nomlabofusp · 1 trial · 2 indications

Phase 3 1
NCT07778836A Study to Evaluate the Efficacy and Safety of Subcutaneous Nomlabofusp in Subjects With Friedreich's AtaxiaFriedreich Ataxia
RECRUITING150 Analytics
PHASE3RECRUITING
A Study to Evaluate the Efficacy and Safety of Subcutaneous Nomlabofusp in Subjects With Friedreich's Ataxia
Friedreich AtaxiaUnlock trial analytics

Study Endpoints

Primary Endpoints

Change from baseline in Upright Stability Score (USS) subscale E of modified Friedreich's Ataxia Rating Scale (mFARS) at Week 72 (Region-specific)
Baseline, Weeks 12, 24, 36, 48, 72

Number - The USS has a score range from 0 to 36. Lower scores mean less impairment and higher scores mean greater neurological impairment.

Change from baseline in the total modified Friedreich's Ataxia Rating Scale (mFARS) at Week 72 (Region-specific)
Baseline, Weeks 12, 24, 36, 48, 72

Number - The mFARS has a total score range from 0 to 93. Lower scores mean less impairment and higher scores mean greater neurological impairment.

Secondary Endpoints

Change from baseline in the Clinical Global Impression-Severity (CGI-S) score at Week 72
Baseline, Weeks 12, 24, 36, 48, 72
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Study Design & Arms

AllocationRANDOMIZED
MaskingQUADRUPLE
ModelPARALLEL
PurposeTREATMENT

Treatment Arms

ArmTypeDescription
NomlabofuspEXPERIMENTALDaily subcutaneous injection of nomlabofusp for 72 weeks
PlaceboPLACEBO_COMPARATORDaily subcutaneous injection of placebo for 72 weeks

Interventions

NameTypeDescription
NomlabofuspDRUGNomlabofusp is a recombinant fusion protein provided in a sterile, preservative-free buffered solution for subcutaneous injection intended to deliver human frataxin, the protein deficient in Friedreich's ataxia.
PlaceboDRUGThe placebo is a sterile, preservative-free, clear liquid for subcutaneous injection.
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Eligibility Criteria

Age Range12 Years to 40 Years
SexALL
Healthy VolunteersNo
Study Sites3

Key Inclusion Criteria: Subjects who meet all of the following criteria are potentially eligible for study participation: 1. Subject must provide genetically confirmed FRDA diagnosis report and is homozygous for GAA repeat expansions documented on the genetic diagnostic report, with repeat sizing ...

Countries:United States
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Recent Changes (Last 90 Days)

LOWAug 31, 2026NCT07778836lastUpdatePostDate: changed
LOWAug 31, 2026NCT07778836lastUpdatePostDate: changed
LOWAug 21, 2026NCT07778836NEW_TRIAL: changed
LOWAug 21, 2026NCT07778836NEW_TRIAL: changed

Frequently asked questions about Nomlabofusp

What is Nomlabofusp used for in Friedreich Ataxia?

Nomlabofusp is an investigational small molecule being developed for the treatment of Friedreich Ataxia, a rare inherited disease that affects coordination, muscle strength, and other functions. It is administered by subcutaneous injection and is currently in Phase 3 clinical development.

What does Nomlabofusp target?

Nomlabofusp targets the underlying cause of Friedreich Ataxia by addressing frataxin deficiency, the molecular defect responsible for the disease. It is designed to restore frataxin levels, which are critically low in patients with this condition.

Who makes Nomlabofusp?

Nomlabofusp is being developed by Larimar Therapeutics, Inc., a biopharmaceutical company traded on the Nasdaq under the ticker symbol LRMR. The company is focused on advancing this therapy for patients with Friedreich Ataxia.

What phase is Nomlabofusp in?

Nomlabofusp is currently in Phase 3 clinical development. It has received several FDA designations, including Breakthrough Therapy, Accelerated Approval, Orphan Drug, Rare Pediatric Disease, and Fast Track, reflecting its potential to address a serious unmet medical need.

What clinical trials is Nomlabofusp in?

Nomlabofusp is being evaluated in a Phase 3 clinical trial with the identifier NCT07778836. This randomized, double-blind, placebo-controlled study is recruiting approximately 150 participants aged 12 years and older with Friedreich Ataxia in the United States.

Is Nomlabofusp FDA approved?

Nomlabofusp is not FDA approved. It is an investigational drug currently in Phase 3 clinical trials, meaning it has not yet received marketing authorization. Its FDA designations, including Breakthrough Therapy and Fast Track, are intended to expedite its development and review.