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obudanersen

Phase 3

Angelman Syndrome | Small molecule | Rare Disease |Ionis Pharmaceuticals, Inc.|Last Updated: Aug 28, 2026

Success Probability

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Trial Design

RandomizedDouble-BlindPLACEBO_CONTROLLEDDMC
Total Trials2
Total Enrollment188

FDA Designations

No designations recorded

Clinical trial landscape

obudanersen · 2 trials · 1 indication

Phase 3 2
NCT07782827CHAMPION: A Study to Evaluate the Efficacy and Safety of Obudanersen (ION582) in Children and Adults With Angelman Syndrome (AS)Angelman Syndrome
NOT YET_RECRUITING30 Analytics
NCT06914609REVEAL: A Phase 3 Study of Obudanersen (ION582) in Angelman SyndromeAngelman Syndrome
RECRUITING158 Analytics
PHASE3NOT YET_RECRUITING
CHAMPION: A Study to Evaluate the Efficacy and Safety of Obudanersen (ION582) in Children and Adults With Angelman Syndrome (AS)
Angelman SyndromeUnlock trial analytics
PHASE3RECRUITING
REVEAL: A Phase 3 Study of Obudanersen (ION582) in Angelman Syndrome
Angelman SyndromeUnlock trial analytics

Study Endpoints

Primary Endpoints

Change From Baseline in Performance on the Expressive Communication Domain Raw Score Without Caregiver Input of the Bayley Scales for Infant and Toddler Development-4 (Bayley-4) in Cohort 1
Baseline and Week 52
Change in Performance on the Expressive Communication Subdomain Raw Score of the Bayley Scales for Infant and Toddler Development-4 (Bayley-4) Without Caregiver Input in Cohort 1
Baseline and Week 52

The Bayley-4 is a performance-based assessment of developmental functioning across communication, cognition, and motor skills. The expressive communication subdomain of communication measures preverbal and verbal communication. The total raw score reflects the sum of all the item scores within the expressive communication subdomain, with higher scores reflecting greater expressive communication ability.

Secondary Endpoints

Change From Baseline in Bayley-4: Cognition Scale Raw Score Without Caregiver Input
Baseline and Week 52
Change From Baseline in Aberrant Behavior Checklist - Second Edition - Community Version (ABC-2-C): Hyperactivity
Baseline and Week 52
Change From Baseline in (ABC-2-C): Irritability
Baseline and Week 52
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Study Design & Arms

AllocationNA
MaskingNONE
ModelSINGLE_GROUP
PurposeTREATMENT

Treatment Arms

ArmTypeDescription
obudanersen 80 mgEXPERIMENTALParticipants in Cohorts 1 and 2 will be administered obudanersen via intrathecal (IT) bolus injection every 12 weeks during the Treatment Evaluation and LTE periods.
Cohort 1 obudanersen 80 mgEXPERIMENTALParticipants (aged 2 to \<18 years old) will be administered obudanersen 80 mg via intrathecal (IT) injection every 12 weeks during the double blind and LTE treatment periods.
Cohort 1 PlaceboPLACEBO_COMPARATORParticipants (aged 2 to \<18 years old) will be administered obudanersen matching placebo via IT injection every 12 weeks during the double-blind treatment period and then administered obudanersen 40 mg or 80 mg every 12 weeks during the LTE treatment period.
Cohort 2 obudanersen 80 mgEXPERIMENTALParticipants (aged 18 to ≤50 years old) will be administered obudanersen 80 mg via IT injection every 12 weeks during the double blind and LTE treatment periods.
Cohort 2 PlaceboPLACEBO_COMPARATORParticipants (aged 18 to ≤50 years old) will be administered obudanersen matching placebo via IT injection every 12 weeks during the double-blind treatment period and then randomized to obudanersen 40 mg or 80 mg every 12 weeks during the LTE treatment period.

Interventions

NameTypeDescription
obudanersenDRUGION582 will be administered by IT injection.
PlaceboDRUGobudanersen matching placebo will be administered by IT injection.
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Eligibility Criteria

Age Range2 Years to 50 Years
SexALL
Healthy VolunteersNo

Key Inclusion Criteria: 1. Clinical diagnosis of AS with molecular result indicating either paternal UPD of 15q11.2-q13 or ID of the maternal 15q11.2-q13 region, provided by the Investigator and confirmed by either a qualified central vendor or a qualified local geneticist at the site. 2. The parti...

Countries:United StatesAustraliaCanadaGermanyIsraelItalyJapanPolandSingaporeSouth KoreaSpainUnited Kingdom
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Recent Changes (Last 90 Days)

LOWAug 28, 2026NCT06914609lastUpdatePostDate: changed
LOWAug 28, 2026NCT06914609lastUpdatePostDate: changed
LOWAug 24, 2026NCT07782827NEW_TRIAL: changed
LOWAug 24, 2026NCT07782827NEW_TRIAL: changed
MEDIUMAug 12, 2026NCT06914609lastUpdatePostDate: changed
MEDIUMAug 12, 2026NCT06914609lastUpdatePostDate: changed
LOWJul 29, 2026NCT06914609lastUpdatePostDate: changed
LOWJul 29, 2026NCT06914609lastUpdatePostDate: changed
LOWJun 23, 2026NCT06914609lastUpdatePostDate: changed
LOWJun 23, 2026NCT06914609lastUpdatePostDate: changed

Frequently asked questions about obudanersen

What is obudanersen used for?

Obudanersen is an investigational small molecule being developed for Angelman Syndrome, a rare genetic disorder. It is currently in Phase 3 clinical trials. The drug is designed to address the underlying cause of the condition, though the specific mechanism is not detailed here.

Who makes obudanersen?

Obudanersen is being developed by Ionis Pharmaceuticals, Inc., a biopharmaceutical company traded on NASDAQ under the ticker symbol IONS. The company is conducting Phase 3 clinical trials to evaluate the drug's efficacy and safety in patients with Angelman Syndrome.

What phase is obudanersen in?

Obudanersen is in Phase 3 clinical development. It is not yet approved by regulatory authorities and remains investigational. Two Phase 3 trials are ongoing or planned, with a combined enrollment of 188 participants, to assess its effects in Angelman Syndrome.

What clinical trials is obudanersen in?

Obudanersen is being studied in two Phase 3 trials. The REVEAL study (NCT06914609) is recruiting 158 participants across multiple countries, while the CHAMPION study (NCT07782827) is not yet recruiting and plans to enroll 30 participants. Both trials are placebo-controlled and double-blind.

Is obudanersen the same as ION582?

Obudanersen is also known as ION582, as indicated in the clinical trial titles. Both names refer to the same investigational drug being developed by Ionis Pharmaceuticals for Angelman Syndrome. The trials use the ION582 designation in their official titles.