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ISIS 333611

Phase 1

Familial Amyotrophic Lateral Sclerosis | Small molecule | Neurology |Ionis Pharmaceuticals, Inc.|Last Updated: Apr 13, 2012

Success Probability
Approval Probability 71%
TA Base Rate26%
Adjusted LOA41%
ML RiskLOW_RISK
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Market & Valuation
rNPV $3.2B
Market Size $9.4B
Revenue Basis $1.6B
Competitors 6
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Trial Design
RandomizedDouble-BlindPLACEBO_CONTROLLEDDMCBiomarker
Total Trials1
Total Enrollment33
FDA Designations
No designations recorded
Clinical Trials (1)
NCT IDTitlePhaseStatusEnrollmentVelocityDesignStartCompletionLast UpdatedSitesCountries
NCT01041222Safety, Tolerability, and Activity Study of ISIS SOD1Rx to Treat Familial Amyotrophic Lateral Sclerosis (ALS) Caused by SOD1 Gene MutationsPHASE1 COMPLETED 33Jan 1, 2010Jan 1, 2012Apr 13, 20124 United States
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Study Endpoints
Primary Endpoints
To evaluate the safety, tolerability, and pharmacokinetics of four dose levels of ISIS 333611
Safety analysis for dose escalation after Study Day 8
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Study Design & Arms
AllocationRANDOMIZED
MaskingQUADRUPLE
ModelPARALLEL
PurposeTREATMENT
Treatment Arms
ArmTypeDescription
Arm 1EXPERIMENTAL0.15 mg ISIS 333611 continuous intrathecal infusion over 12 hours
Arm 2EXPERIMENTAL0.5 mg ISIS 333611 continuous intrathecal infusion over 12 hours
Arm 3EXPERIMENTAL1.5 mg ISIS 333611 continuous intrathecal infusion over 12 hours
Arm 4EXPERIMENTAL3.0 mg ISIS 333611 continuous intrathecal infusion over 12 hours
Placebo (phosphate buffered saline)PLACEBO_COMPARATOR -
Interventions
NameTypeDescription
ISIS 333611DRUG5 arms of 12 hour infusion: Arm 1 0.15 mg, Arm 2 0.5 mg, Arm 3 1.5 mg, Arm 4 3.0 mg, matching volume of placebo
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Eligibility Criteria
Age Range18 Years — N/A
SexALL
Healthy VolunteersNo
Study Sites4

Inclusion Criteria: * Clinical signs of weakness attributed to ALS. * Familial ALS with a documented SOD1 gene mutation. * Age 18 years or older. * Capable of providing informed consent and willing to comply with trial procedures and time commitments. * Vital capacity (VC) at least 50% predicted va...

Countries:United States
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