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ION717

Phase 1

Prion Disease | Small molecule | Other |Ionis Pharmaceuticals, Inc.|Last Updated: Apr 24, 2026

Success Probability
Approval Probability 71%
TA Base Rate26%
Adjusted LOA41%
ML RiskLOW_RISK
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Market & Valuation
rNPV $3.2B
Market Size $9.4B
Revenue Basis $1.6B
Competitors 6
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Trial Design
RandomizedDouble-BlindCONTROLLED
Total Trials1
Total Enrollment76
FDA Designations
No designations recorded
Clinical Trials (1)
NCT IDTitlePhaseStatusEnrollmentVelocityDesignStartCompletionLast UpdatedSitesCountries
NCT06153966PrProfile: A Study to Assess the Safety, Tolerability, Pharmacokinetics and Pharmacodynamics of ION717PHASE1 RECRUITING 76Jan 4, 2024Jun 1, 2030Apr 24, 202613 United States, Australia +7
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Study Endpoints
Primary Endpoints
Incidence of treatment-emergent adverse events.
Baseline up to Week 33
Secondary Endpoints
Maximum Observed Plasma Concentration (Cmax) of ION717
on Day 1 and Week 9
Area Under the Plasma Concentration-time Curve (AUC) of ION717
on Day 1 and Week 9
Half-life (t1/2λz) of ION717 in Plasma
on Day 1 and Week 9
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Study Design & Arms
AllocationRANDOMIZED
MaskingDOUBLE
ModelPARALLEL
PurposeTREATMENT
Treatment Arms
ArmTypeDescription
ION717 + Placebo, Regimen 1EXPERIMENTALParticipants will receive multiple doses of study drug (ION717 and placebo) during the 30-week treatment period; the order of doses is blinded. Participants will then receive multiple doses of ION717 during the 142-week open-label extension period.
ION717 + Placebo, Regimen 2EXPERIMENTALParticipants will receive multiple doses of study drug (ION717 and placebo) during the 30-week treatment period; the order of doses is blinded. Participants will then receive multiple doses of ION717 during the 142-week open-label extension period.
ION717, Regimen 3EXPERIMENTALParticipants will receive multiple doses of ION717 during the 30-week treatment period and the 142-week open-label extension period.
Interventions
NameTypeDescription
ION717DRUGION717 will be administered by IT injection.
PlaceboDRUGPlacebo-matching ION717 will be administered by IT injection.
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Eligibility Criteria
Age Range18 Years — N/A
SexALL
Healthy VolunteersNo
Study Sites13

Key Inclusion Criteria * A confirmed diagnosis of probable or definite prion disease. * Early-stage prion disease at the time of Screening. * Willing to meet all study requirements, including travel to Study Center, procedures, measurements and visits. * Patients must have a caregiver who is ≥ 18 y...

Countries:United StatesAustraliaCanadaFranceGermanyIsraelItalyJapanSpain
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Recent Changes (Last 90 Days)
LOWMay 26, 2026NCT06153966primaryCompletionDate: changed
LOWMay 24, 2026NCT06153966studyFirstPostDate: changed