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DNL952

Phase 1

Late-onset Pompe Disease | Small molecule | Rare Disease |Denali Therapeutics Inc.|Last Updated: Aug 17, 2026

Target and mechanism

Molecular targetGAA
Target classEnzyme
ModalitySmall molecule

Success Probability

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Market & Valuation

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Trial Design

CONTROLLED
Total Trials1
Total Enrollment32

FDA Designations

No designations recorded

Clinical trial landscape

DNL952 · 1 trial · 1 indication

Phase 1 1
NCT07354724A Study to Evaluate the Safety, Pharmacokinetics, and Pharmacodynamics of DNL952 in Adult Participants With Late-Onset Pompe DiseaseLate-onset Pompe Disease
RECRUITING32 Analytics
PHASE1RECRUITING
A Study to Evaluate the Safety, Pharmacokinetics, and Pharmacodynamics of DNL952 in Adult Participants With Late-Onset Pompe Disease
Late-onset Pompe DiseaseUnlock trial analytics

Study Endpoints

Primary Endpoints

Incidence, severity, and seriousness of treatment-emergent adverse events (TEAEs)
48 weeks
Incidence and severity of infusion-related reacations (IRRs)
48 weeks

Secondary Endpoints

PK parameter: Maximum concentration (Cmax) of DNL952 in serum
48 weeks
PK Parameter: Time to reach maximum concentration (tmax) of DNL952 in serum
48 weeks
PK Parameter: Area under the concentration-time curve (AUC) from time zero to time of last measurable concentration (AUClast) of DNL952 in serum
48 weeks
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Study Design & Arms

AllocationNON_RANDOMIZED
MaskingNONE
ModelSEQUENTIAL
PurposeTREATMENT

Treatment Arms

ArmTypeDescription
Cohort A1EXPERIMENTALParticipants with LOPD
Cohort A2EXPERIMENTALParticipants with LOPD
Cohort A3 (Optional)EXPERIMENTALParticipants with LOPD
Cohort A4 (Optional)EXPERIMENTALParticipants with LOPD
Cohort B1 (Optional)EXPERIMENTALParticipants with LOPD
Cohort B2 (Optional)EXPERIMENTALParticipants with LOPD

Interventions

NameTypeDescription
DNL952DRUGIntravenous repeating dose
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Eligibility Criteria

Age Range18 Years to 75 Years
SexALL
Healthy VolunteersNo
Study Sites4

Key Inclusion Criteria: * Body weight ≥40 kg * Diagnosis of LOPD * Upright FVC ≥ 30% of predicted normal value * Able to ambulate ≥ 40 meters (use of assistive devices is acceptable) * \[Cohorts A1-A4 only\] Have received avalglucosidase alfa or cipaglucosidase alfa at a dose of 20 mg/kg every 2 we...

Countries:United States
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Recent Changes (Last 90 Days)

LOWAug 17, 2026NCT07354724lastUpdatePostDate: changed
LOWAug 17, 2026NCT07354724lastUpdatePostDate: changed
LOWJun 29, 2026NCT07354724startDate: changed
LOWJun 29, 2026NCT07354724startDate: changed

Frequently asked questions about DNL952

What is DNL952 used for in Late-Onset Pompe Disease?

DNL952 is an investigational small molecule being developed for the treatment of late-onset Pompe disease, a rare genetic disorder. It is currently in Phase 1 clinical development and has not been approved by regulatory authorities. The drug is being studied in adult participants with this condition.

What does DNL952 target?

DNL952 targets GAA, which is an enzyme. In late-onset Pompe disease, deficiencies in GAA activity lead to glycogen accumulation. By targeting this enzyme, DNL952 aims to address the underlying pathology of the disease. The drug is a small molecule designed to modulate GAA function.

Who makes DNL952?

DNL952 is being developed by Denali Therapeutics Inc., a biopharmaceutical company. Denali is publicly traded under the ticker symbol DNLI. The company is conducting clinical trials to evaluate the safety, pharmacokinetics, and pharmacodynamics of DNL952 in patients with late-onset Pompe disease.

What phase is DNL952 in?

DNL952 is in Phase 1 clinical development. It is an investigational drug and has not yet been approved by the FDA or other regulatory bodies. The ongoing Phase 1 trial is recruiting participants to assess the drug's safety, pharmacokinetics, and pharmacodynamics in adults with late-onset Pompe disease.

What clinical trials is DNL952 in?

DNL952 is being evaluated in a Phase 1 clinical trial with the identifier NCT07354724. This study is titled 'A Study to Evaluate the Safety, Pharmacokinetics, and Pharmacodynamics of DNL952 in Adult Participants With Late-Onset Pompe Disease.' The trial is currently recruiting 32 participants in the United States and is controlled but not randomized or double-blinded.