Recent Updates
Recently added Catalysts

PRO044

Phase 1

Duchenne Muscular Dystrophy | Small molecule | Neurology |BioMarin Pharmaceutical Inc.|Last Updated: Oct 16, 2018

Success Probability
Approval Probability 71%
TA Base Rate26%
Adjusted LOA41%
ML RiskLOW_RISK
Premium
Market & Valuation
rNPV $3.2B
Market Size $9.4B
Revenue Basis $1.6B
Competitors 6
Premium
Trial Design
CONTROLLEDDMCBiomarker
Total Trials1
Total Enrollment18
FDA Designations
No designations recorded
Clinical Trials (1)
NCT IDTitlePhaseStatusEnrollmentVelocityDesignStartCompletionLast UpdatedSitesCountries
NCT01037309Phase I/II Study of PRO044 in Duchenne Muscular Dystrophy (DMD)PHASE1 COMPLETED 18Dec 1, 2009Oct 1, 2013Oct 16, 20184 Belgium, Italy +2
Unlock Drug Trial Details
Study Endpoints
Primary Endpoints
Increase in Dystrophin Expression in the Muscle Biopsies by Immunofluorescence Analyses of Cross-sections and by Western Blot Analyses of Total Protein Extracts
Within 13 weeks after 5 weeks of treatment
Safety and Tolerability of PRO044
During the 5 weeks of treatment and during the 13 weeks after treatment

number of subjects with 1 or more treatment emergent adverse events following SC or IV PRO044

Secondary Endpoints
PRO044 Pharmacokinetic Cmax (μg/mL) Following Subcutaneous Administration
Week 1, Week 5
Unlock Study Endpoints
Study Design & Arms
AllocationNON_RANDOMIZED
MaskingNONE
ModelPARALLEL
PurposeTREATMENT
Treatment Arms
ArmTypeDescription
PRO044, cohort 1EXPERIMENTALSubcutaneous injection of 0.5 mg/kg on day 1, 8, 15, 22 and 29.
PRO044, cohort 2EXPERIMENTALSubcutaneous injection of maximally 1.5 mg/kg on day 1, 8, 15, 22 and 29.
PRO044, cohort 3EXPERIMENTALSubcutaneous injection of maximally 5 mg/kg on day 1, 8, 15, 22 and 29.
PRO044, cohort 4EXPERIMENTALSubcutaneous injection of maximally 8 mg/kg on day 1, 8, 15, 22 and 29.
PRO044, cohort 5EXPERIMENTALSubcutaneous injection of maximally 10 mg/kg on day 1, 8, 15, 22 and 29
PRO044, cohort 6EXPERIMENTALSubcutaneous injection of maximally 12 mg/kg on day 1, 8, 15, 22 and 29
PRO044, cohort 7EXPERIMENTALIntravenous injection of maximally 1.5 mg/kg on day 1, 8, 15, 22 and 29
PRO044, cohort 8EXPERIMENTALIntravenous injection of maximally 5 mg/kg on day 1, 8, 15, 22 and 29
PRO044, cohort 9EXPERIMENTALIntravenous injection of maximally 8 mg/kg on day 1, 8, 15, 22 and 29
Interventions
NameTypeDescription
PRO044 SCDRUGSubcutaneous injection, once a week, for five weeks
PRO044 IVDRUGIntravenous injection, once a week, for five weeks
Unlock Study Design Details
Eligibility Criteria
Age Range5 Years — 16 Years
SexMALE
Healthy VolunteersNo
Study Sites4

Inclusion Criteria: 1. Boys aged between 5 and 16 years inclusive. 2. Duchenne muscular dystrophy resulting from a mutation correctable by treatment with PRO044. 3. Life expectancy of at least 6 months. 4. No previous treatment with investigational medicinal treatment within 6 months prior to the s...

Countries:BelgiumItalyNetherlandsSweden
Unlock Eligibility Criteria