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BMN 701

Phase 1

Pompe Disease | Monoclonal antibody | Metabolic |BioMarin Pharmaceutical Inc.|Last Updated: Jun 11, 2018

Success Probability
Approval Probability 71%
TA Base Rate26%
Adjusted LOA41%
ML RiskLOW_RISK
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Market & Valuation
rNPV $3.2B
Market Size $9.4B
Revenue Basis $1.6B
Competitors 6
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Trial Design
UNCONTROLLEDDMCBiomarker
Total Trials1
Total Enrollment22
FDA Designations
No designations recorded
Clinical Trials (1)
NCT IDTitlePhaseStatusEnrollmentVelocityDesignStartCompletionLast UpdatedSitesCountries
NCT01230801Safety/Tolerability/Pharmacokinetic (PK)/Pharmacodynamics (PD) Study of BMN701 in Patients With Late-Onset Pompe DiseasePHASE1 COMPLETED 22Jan 17, 2011Mar 6, 2013Jun 11, 201810 United States, Australia +3
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Study Endpoints
Primary Endpoints
Number of Participants With Adverse Events
24 weeks

Number of Participants with Adverse Events as a Measure of Safety and Tolerability

Secondary Endpoints
Change From Baseline in Six Minutes Walk Test
Baseline up to 24 weeks
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Study Design & Arms
AllocationNA
MaskingNONE
ModelSINGLE_GROUP
PurposeTREATMENT
Treatment Arms
ArmTypeDescription
BMN 701EXPERIMENTALIV infusion
Interventions
NameTypeDescription
BMN 701BIOLOGICALGILT-tagged recombinant human GAA
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Eligibility Criteria
Age Range13 Years — N/A
SexALL
Healthy VolunteersNo
Study Sites10

Inclusion criteria: * Patient has been diagnosed with Pompe Disease prior to or during the screening period based on 2 GAA gene mutations and either: endogenous GAA activity \<75% of the lower limit of the normal adult range reported by the testing laboratory, as assessed in cultured skin fibroblas...

Countries:United StatesAustraliaFranceGermanyUnited Kingdom
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