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BMN 349

Phase 1

Alpha 1-Antitrypsin Deficiency | Small molecule | Other |BioMarin Pharmaceutical Inc.|Last Updated: May 6, 2026

Success Probability
Approval Probability 71%
TA Base Rate26%
Adjusted LOA41%
ML RiskLOW_RISK
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Market & Valuation
rNPV $3.2B
Market Size $9.4B
Revenue Basis $1.6B
Competitors 6
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Trial Design
RandomizedDouble-BlindCONTROLLEDBiomarker
Total Trials1
Total Enrollment6
FDA Designations
No designations recorded
Clinical Trials (1)
NCT IDTitlePhaseStatusEnrollmentVelocityDesignStartCompletionLast UpdatedSitesCountries
NCT06738017Study of BMN 349 Single Dose in PiZZ and PiMZ/MASH Adult ParticipantsPHASE1 ACTIVE NOT_RECRUITING 6Feb 21, 2025Aug 19, 2026May 6, 20267 United States, United Kingdom
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Study Endpoints
Primary Endpoints
Participant Adverse Events, Serious Adverse Events, Dose Limit Toxicities, Adverse Event of Special Interests, abnormal laboratory tests, abnormal pulmonary function tests, and 12-lead ECG parameters
78 days

Number of participant AEs, SAEs, DLTs, AESIs per physician's assessment, abnormal laboratory tests through whole blood samples, abnormal pulmonary function spirometry tests, and 12-lead ECG parameters changes from baseline following a single oral dose of BMN 349

Secondary Endpoints
C max
78 days
AUC 0-t
78 days
AUC 0-inf
78 days
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Study Design & Arms
AllocationRANDOMIZED
MaskingTRIPLE
ModelPARALLEL
PurposeTREATMENT
Treatment Arms
ArmTypeDescription
Group A (PiZZ)OTHER5:1 (349:Placebo)
Group B (PiMZ)OTHER5:1 (349:Placebo)
Interventions
NameTypeDescription
BMN 349DRUG250mg oral tablet
PlaceboDRUG250mg oral tablet
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Eligibility Criteria
Age Range18 Years — 75 Years
SexALL
Healthy VolunteersNo
Study Sites7

Inclusion Criteria: * Participants must have confirmation of PiZZ or PiMZ genotype * Females and males, of any race, 18 to 75 years of age * Nonsmokers, defined as not using tobacco or nicotine-containing products for at least 6 months prior to Screening Exclusion Criteria: * International normal...

Countries:United StatesUnited Kingdom
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Recent Changes (Last 90 Days)
HIGHMay 26, 2026NCT06738017Status: RECRUITING → ACTIVE_NOT_RECRUITING
LOWMay 24, 2026NCT06738017studyFirstPostDate: changed