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BMN 110- Weekly

Phase 3

Mucopolysaccharidosis IV A | Small molecule | Rare Disease |BioMarin Pharmaceutical Inc.|Last Updated: Jul 21, 2021

Success Probability

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Trial Design

RandomizedDouble-BlindCONTROLLEDDMC
Total Trials1
Total Enrollment173

FDA Designations

No designations recorded

Clinical trial landscape

BMN 110- Weekly · 1 trial · 3 indications

Phase 3 1
NCT01415427Long-Term Efficacy and Safety Extension Study of BMN 110 in Patients With Mucopolysaccharidosis IVA (Morquio A Syndrome)Mucopolysaccharidosis IV A
COMPLETED173 Analytics
PHASE3COMPLETED
Long-Term Efficacy and Safety Extension Study of BMN 110 in Patients With Mucopolysaccharidosis IVA (Morquio A Syndrome)
Mucopolysaccharidosis IV AUnlock trial analytics

Study Endpoints

Primary Endpoints

Change From Baseline in 6-minute Walk (6MW) Test - ITT
Baseline to week 168

Efficacy was assessed by changes from baseline in 6-minute walk test

Change From Baseline in 6-minute Walk (6MW) Test - MPP
Baseline to week 168

Efficacy was assessed by changes from baseline in 6-minute walk test

Secondary Endpoints

Change From Baseline in 3-minute Stair Climb Test - ITT
Baseline to week 168
Change From Baseline in 3-minute Stair Climb Test - MPP
Baseline to week 168
Change From Baseline in Urine Keratan Sulfate - ITT
Baseline to week 168
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Study Design & Arms

AllocationRANDOMIZED
MaskingQUADRUPLE
ModelPARALLEL
PurposeTREATMENT

Treatment Arms

ArmTypeDescription
BMN 110 WeeklyEXPERIMENTALBMN 110 Weekly: In Part 1, patients will receive an intravenous infusion of BMN 110 at a dose of 2.0 mg/kg administered over a period of approximately 4 hours once a week.
BMN 110 Every Other WeekEXPERIMENTALBMN 110 Every Other Week: In Part 1, patients will receive an intravenous infusion of BMN 110 at a dose of 2.0 mg/kg administered over a period of approximately 4 hours every other week and will receive infusions of placebo on alternating weeks.

Interventions

NameTypeDescription
BMN 110 - WeeklyDRUGIn Part 1, patients will receive intravenous (IV) infusions of study drug at a dose of 2.0 mg/kg/qw administered over a period of approximately 4 hours once a week. In Part 2, patients will continue to receive 2.0 mg/kg of BMN 110 every week, with no placebo.
BMN 110 - Every Other WeekDRUGIn Part 1, patients will receive intravenous (IV) infusions of study drug at a dose of 2.0 mg/kg administered over a period of approximately 4 hours every other week. Patients randomized to the 2.0 mg/kg/qow arm will receive infusions of placebo on alternating weeks, to mask active drug weeks. In Part 2, patients will receive 2.0 mg/kg of BMN 110 every week, with no placebo.
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Eligibility Criteria

Age Range5 Years to N/A
SexALL
Healthy VolunteersNo
Study Sites43

Inclusion Criteria: * Must have completed MOR-004 * Is willing and able to provide written, signed informed consent. Or in the case of patients under the age of 18 (or other age as defined by regional law or regulation), provide written assent (if required) and have written informed consent, signed...

Countries:United StatesArgentinaBrazilCanadaColombiaDenmarkFranceGermanyItalyJapanNetherlandsNorwayPortugalQatarSaudi ArabiaSouth KoreaSpainTaiwanTurkey (Türkiye)United Kingdom
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Frequently asked questions about BMN 110- Weekly

What is BMN 110 Weekly used for in MPS IV A?

BMN 110 Weekly is an investigational small molecule being studied for the treatment of Mucopolysaccharidosis IV A (MPS IV A), also known as Morquio A syndrome. It is developed by BioMarin Pharmaceutical Inc. (BMRN) and is currently in Phase 3 clinical development for this rare disease indication.

What does BMN 110 Weekly target?

BMN 110 Weekly is a small molecule therapy. The specific molecular target of BMN 110 Weekly is not disclosed in the available clinical trial information. The drug is being evaluated for its efficacy and safety in patients with Mucopolysaccharidosis IV A (Morquio A syndrome).

Who makes BMN 110 Weekly?

BMN 110 Weekly is developed by BioMarin Pharmaceutical Inc., a biopharmaceutical company traded on the NASDAQ under the ticker symbol BMRN. BioMarin is conducting Phase 3 clinical trials to evaluate the drug for the treatment of Mucopolysaccharidosis IV A (Morquio A syndrome).

What phase is BMN 110 Weekly in?

BMN 110 Weekly is in Phase 3 clinical development. It is an investigational drug and has not been approved by regulatory authorities. Two Phase 3 trials have been completed, including a double-blind, placebo-controlled study and a long-term extension study, both in patients with MPS IV A.

What clinical trials is BMN 110 Weekly in?

BMN 110 Weekly has been studied in two completed Phase 3 trials. The first, NCT01275066, was a double-blind, placebo-controlled study in 177 patients with MPS IV A. The second, NCT01415427, was a long-term extension study enrolling 173 patients. Both trials included patients aged 5 years and older across multiple countries.

Is BMN 110 Weekly the same as elosulfase alfa?

BMN 110 Weekly is the investigational name for the drug also known as elosulfase alfa. It is developed by BioMarin Pharmaceutical Inc. for the treatment of Mucopolysaccharidosis IV A (Morquio A syndrome). The drug has been evaluated in Phase 3 clinical trials under the name BMN 110.