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BMN 110 Weekly

Phase 3

MPS IV A | Small molecule | Other |BioMarin Pharmaceutical Inc.|Last Updated: Jul 7, 2014

Success Probability
Approval Probability 71%
TA Base Rate26%
Adjusted LOA41%
ML RiskLOW_RISK
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Market & Valuation
rNPV $3.2B
Market Size $9.4B
Revenue Basis $1.6B
Competitors 6
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Trial Design
RandomizedDouble-BlindPLACEBO_CONTROLLEDDMCBiomarker
Total Trials1
Total Enrollment177
FDA Designations
No designations recorded
Clinical Trials (1)
NCT IDTitlePhaseStatusEnrollmentVelocityDesignStartCompletionLast UpdatedSitesCountries
NCT01275066A Double-Blind Study to Evaluate the Efficacy and Safety of BMN 110 in Patients With Mucopolysaccharidosis IVA (Morquio A Syndrome)PHASE3 COMPLETED 177Feb 1, 2011Aug 1, 2012Jul 7, 201428 United States, Argentina +15
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Study Endpoints
Primary Endpoints
Change From Baseline in Endurance as Measured by the 6-minute Walk Test
Baseline to Week 24
Secondary Endpoints
Change From Baseline in Endurance as Measured by the 3-minute Stair Climb Test
Baseline to Week 24
Percent Change From Baseline in Urine Keratan Sulfate Normalized for Urine Creatinine
Baseline to Week 24
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Study Design & Arms
AllocationRANDOMIZED
MaskingQUADRUPLE
ModelPARALLEL
PurposeTREATMENT
Treatment Arms
ArmTypeDescription
PlaceboPLACEBO_COMPARATOR -
BMN 110 WeeklyEXPERIMENTAL -
BMN 110 Every Other WeekEXPERIMENTAL -
Interventions
NameTypeDescription
BMN 110 WeeklyDRUGBMN 110 Weekly: Intravenous infusion of BMN 110 at a dose of 2.0 mg/kg administered over a period of approximately 4 hours once a week.
PlaceboDRUGIntravenous infusion of placebo solution at a volume equivalent to that needed for 2.0 mg/kg dose of BMN 110 administered over a period of approximately 4 hours once a week.
BMN 110 Every Other WeekDRUGBMN 110 Every Other Week: Intravenous infusion of BMN 110 at a dose of 2.0 mg/kg administered over a period of approximately 4 hours every other week and infusions of placebo on alternating weeks.
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Eligibility Criteria
Age Range5 Years — N/A
SexALL
Healthy VolunteersNo
Study Sites28

Inclusion Criteria: * At least 5 years of age. * Documented clinical diagnosis of MPS IVA based on clinical signs and symptoms of MPS IVA and documented reduced fibroblast or leukocyte GALNS enzyme activity or genetic testing confirming diagnosis of MPS IVA. * Willing and able to provide written, s...

Countries:United StatesArgentinaBrazilCanadaColombiaDenmarkFranceGermanyItalyJapanNetherlandsPortugalQatarSaudi ArabiaSouth KoreaTaiwanUnited Kingdom
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