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BMN 110

Phase 3

Mucopolysaccharidosis IVA (Morquio A Syndrome) | Small molecule | Rare Disease |BioMarin Pharmaceutical Inc.|Last Updated: Sep 26, 2019

Success Probability

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Market & Valuation

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Trial Design

UNCONTROLLEDDMC
Total Trials1
Total Enrollment13

FDA Designations

No designations recorded

Clinical trial landscape

BMN 110 · 3 trials · 5 indications

Phase 3 1Phase 2 1Phase 1 1
NCT01966029BMN 110 Phase 3B in Australian PatientsMucopolysaccharidosis IVA (Morquio A Syndrome)
COMPLETED13 Analytics
PHASE3COMPLETED
BMN 110 Phase 3B in Australian Patients
Mucopolysaccharidosis IVA (Morquio A Syndrome)Unlock trial analytics

Study Endpoints

Primary Endpoints

Safety Analysis
The study period during which all non-serious AEs and SAEs will be reported begins after informed consent is obtained and through 30 days after the last study visit or 30 days after the last drug infusion, whichever comes first.

The analyses of safety will include all patients who receive any study drug. All safety data will be summarized descriptively. All AEs will be coded using the Medical Dictionary for Regulatory Activities (MedDRA). The incidence of AEs will be summarized by System Organ Class (SOC), Preferred Term (PT), relationship to study drug, and severity. Patient listings will be provided for SAEs, deaths, and AEs leading to study drug discontinuation, or study withdrawals. All AE summaries will include only treatment-emergent AEs (TEAEs) reported during the study period (AEs that occur after the first study drug infusion). Infusion-associated AEs will be summarized by SOC, PT and severity. The following safety measures will be summarized descriptively: concomitant medications, clinical laboratory tests, vital signs, ECGs, immunogenicity results, analgesic medication use, results from routine physical examinations (including standard neurologic examinations), and cervical spine imaging.

To Evaluate Safety and Tolerability of Infusions of BMN 110 at a Dose of 2.0 mg/kg/Week Over a 52-week Period in MPS IVA Subjects Less Than 5 Years of Age at Time of First Study Drug Infusion
52 weeks

Number of Participants Experiencing Adverse Events

Subject Incidence of Treatment Emergent AEs
Entire Study, through week 84

The primary objective of the study was to evaluate the safety of weekly infusions of BMN 110 administered in escalating doses to subjects with MPS IVA. The safety variable incidence of TEAE is summarized.

Secondary Endpoints

Efficacy Analysis
Baseline, Week 25, Week 49 or Early Termination Visit
Efficacy Analysis (recommended)
by Week 24, Week 52 and Early Termination Visit during Extension Phase
Percent Change From Baseline to Week 52 in Urinary Keratan Sulfate Measures
Baseline to Week 52
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Study Design & Arms

AllocationNA
MaskingNONE
ModelSINGLE_GROUP
PurposeTREATMENT

Treatment Arms

ArmTypeDescription
TreatmentEXPERIMENTALAll patients receive treatment with BMN 110
BMN 110 WeeklyEXPERIMENTAL -
BMN 110EXPERIMENTALWithin-patient Dose-Escalation

Interventions

NameTypeDescription
BMN 110DRUGAll pateints receive treatment with BMN 110
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Eligibility Criteria

Age RangeN/A to 5 Years
SexALL
Healthy VolunteersNo
Study Sites5

Inclusion Criteria: 1. Diagnosed with MPS IVA as confirmed by a documented GALNS enzymatic test (GALNS activity in affected range, beta-galactosidase and a second lysosomal sulfatase activity within normal range). 2. Age 12 months or older. 3. Willing and able to provide written, signed informed co...

Countries:AustraliaUnited StatesItalyTaiwanUnited Kingdom
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Frequently asked questions about BMN 110

What is BMN 110 used for?

BMN 110 is used for the treatment of Mucopolysaccharidosis IVA, also known as Morquio A Syndrome. This is a rare genetic disorder. The drug is being developed as a potential therapy for this condition.

Who makes BMN 110?

BMN 110 is being developed by BioMarin Pharmaceutical Inc., a biopharmaceutical company. The company's stock ticker is BMRN. BioMarin is focused on developing therapies for rare diseases.

What phase is BMN 110 in?

BMN 110 is in clinical development. It has completed trials in Phase 1, Phase 2, and Phase 3. However, it is not yet approved and remains an investigational drug. The most advanced completed trial was a Phase 3 study.

What clinical trials is BMN 110 in?

BMN 110 has been studied in several clinical trials. NCT00884949 was a Phase 1 study in the United Kingdom. NCT01515956 was a Phase 2 study in pediatric patients. NCT01966029 was a Phase 3 study in Australia. All trials have been completed.

Is BMN 110 the same as elosulfase alfa?

BMN 110 is also known as elosulfase alfa. It is a drug being developed by BioMarin Pharmaceutical Inc. for the treatment of Mucopolysaccharidosis IVA, also called Morquio A Syndrome.