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Tulmimetostat

Phase 1

Advanced Solid Tumor | Small molecule | Oncology |Novartis AG|Last Updated: Aug 19, 2026

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Trial Design

CONTROLLED
Total Trials1
Total Enrollment300

FDA Designations

No designations recorded

Clinical trial landscape

Tulmimetostat · 3 trials · 12 indications

Phase 1 3
NCT07190300TulmiSTAR-02: A Phase I/II Open-label Study of Tulmimetostat in Combination With Darolutamide vs. Darolutamide, and Tulmimetostat With Abiraterone in Patients With Metastatic Hormone-sensitive Prostate Cancer (mHSPC)Metastatic Hormone-Sensitive Prostate Cancer (mHSPC)
RECRUITING181 Analytics
NCT05944562Tulmimetostat (DZR123) in Patients With Mycosis Fungoides and Sézary SyndromeMycosis Fungoides
ACTIVE NOT_RECRUITING24 Analytics
NCT04104776A Study of Tulmimetostat DZR123 (CPI-0209) in Patients With Advanced Solid Tumors and LymphomasAdvanced Solid Tumor
RECRUITING300 Analytics
PHASE1RECRUITING
TulmiSTAR-02: A Phase I/II Open-label Study of Tulmimetostat in Combination With Darolutamide vs. Darolutamide, and Tulmimetostat With Abiraterone in Patients With Metastatic Hormone-sensitive Prostate Cancer (mHSPC)
Metastatic Hormone-Sensitive Prostate Cancer (mHSPC)Unlock trial analytics
PHASE1ACTIVE NOT_RECRUITING
Tulmimetostat (DZR123) in Patients With Mycosis Fungoides and Sézary Syndrome
Mycosis FungoidesUnlock trial analytics
PHASE1RECRUITING
A Study of Tulmimetostat DZR123 (CPI-0209) in Patients With Advanced Solid Tumors and Lymphomas
Advanced Solid TumorUnlock trial analytics

Study Endpoints

Primary Endpoints

Phase I (Group A and Group B): Dose-limiting toxicities (DLTs)
Up to 28 days

A dose-limiting toxicity is defined as an adverse event or abnormal laboratory value, not clearly due to underlying disease or extraneous causes, that occurs within the first 28 days of treatment with tulmimetostat and meets any of the criteria specified in the protocol. The National Cancer Institute Common Terminology Criteria for Adverse events (NCI CTCAE) version 5.0 will be used for all grading. For the purpose of dose-escalation decisions, DLTs will be considered and included in the Bayesian Logistic Regression Model (BLRM).

Phase I (Group A and Group B): Incidence rate of Adverse Events (AEs) and Serious Adverse Events (SAEs)
From date of randomization till 30 days safety fup, assessed up to approximately 79 months

The analysis of adverse events will include categorization by type, frequency, and severity, as graded by the NCI CTCAE version 5.0.

Phase I (Group A and Group B): Number of Participants with dose adjustments
From date of randomization till 30 days safety fup, assessed up to approximately 79 months

The number of participants with dose adjustments (reductions, interruption, or permanent discontinuation) will be summarized by treatment arm.

Phase I (Group A and Group B): Dose Intensity
From date of randomization till 30 days safety fup, assessed up to approximately 79 months

Dose intensity (computed as the ratio of actual cumulative dose received and actual duration of exposure) and the relative dose intensity (computed as the ratio of dose intensity and planned dose intensity) will be summarized by means of descriptive statistics

Phase I (Group A and Group B): Duration of exposure to each study drug
From date of randomization till 30 days safety fup, assessed up to approximately 79 months

Duration of exposure (in months) to each study drug will be summarized by means of descriptive statistics

Phase II (Group A): Prostate-Specific Antigen (PSA) response rate of < 0.2 ng/mL
From date of randomization till 30 days safety fup, assessed up to approximately 79 months

Prostate-Specific Antigen (PSA) response rate is defined as proportion of participants who achieved a decline in PSA to \< 0.2 ng/mL at month 6 months, confirmed by a second PSA measurement ≥ 3 weeks later.

Frequency and grades of treatment-emergent adverse events (TEAE)
From start of treatment through 30 days after completion of treatment (estimated to be 13 months)
Rate of treatment discontinuation due to treatment-emergent adverse events (TEAE)
From start of treatment through 30 days after completion of treatment (estimated to be 13 months)
Tulmimetostat Monotherapy Phase 1: Frequency of Dose-limiting toxicities (DLTs)
DLTs assessed during Cycle 1 (cycle = 28 days)

The maximum tolerated dose (MTD) and/or recommended phase 2 dose (RP2D) of Tulmimetostat as monotherapy in patients with advanced tumors.

Tulmimetostat Monotherapy Phase 2: Overall response rate (ORR)
Up to 30 months

ORR is defined as the proportion of patients with a best overall response of complete response (CR) or partial response (PR) based on RECIST 1.1 or applicable response criteria

Cohort M8 Part 1: Frequency of Dose-limiting toxicities (DLTs)
DLTs assessed during Cycle 1 (cycle = 28 days)

The maximum tolerated dose (MTD) and/or recommended phase 2 dose (RP2D) of Tulmimetostat in combination with enzalutamide in patients with castration-resistant prostate cancer (mCRPC) with measurable soft tissue disease.

Cohort M8 Part 2: Prostate-Specific Antigen 50 (PSA50) Response
Up to 30 months

Prostate-Specific Antigen 50 (PSA50) is defined as a ≥ 50% decrease in PSA levels from baseline at any timepoint, confirmed by a second PSA measurement ≥ 3 weeks without any PSA progression in between

Secondary Endpoints

Phase I (Group A): Plasma concentrations of Tulmimetostat and Darolutamide
Cycle 1-2: Day 1 (0 hour, 0.5 hours, 1 hour, 2 hours, 3 hours, 4 hours, 6 hours and 8 hours). Cycle 1: Day 2 (Tulmimetostat only: 0 hour and 24 hours), Days 8 and 15 (0 hour and 2 hours). Cycles 3-5: Day 1 (0 hour). 1 cycle = 28 days.
Phase I (Group A): AUC of Tulmimetostat and Darolutamide
Cycle 1-2: Day 1 (0 hour, 0.5 hours, 1 hour, 2 hours, 3 hours, 4 hours, 6 hours and 8 hours). Cycle 1: Day 2 (Tulmimetostat only: 0 hour and 24 hours), Days 8 and 15 (0 hour and 2 hours). Cycles 3-5: Day 1 (0 hour). 1 cycle = 28 days.
Phase I (Group A): Cmax of Tulmimetostat and Darolutamide
Cycle 1-2: Day 1 (0 hour, 0.5 hours, 1 hour, 2 hours, 3 hours, 4 hours, 6 hours and 8 hours). Cycle 1: Day 2 (Tulmimetostat only: 0 hour and 24 hours), Days 8 and 15 (0 hour and 2 hours). Cycles 3-5: Day 1 (0 hour). 1 cycle = 28 days.
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Study Design & Arms

AllocationRANDOMIZED
MaskingQUADRUPLE
ModelPARALLEL
PurposeTREATMENT

Treatment Arms

ArmTypeDescription
Phase I: Group A (part 1)EXPERIMENTALTulmimetostat oral (PO) once a day (QD) escalating doses + Darolutamide 600 mg twice a day (BID)
Phase I: Group B (part 2)EXPERIMENTALTulmimetostat PO QD escalating doses + Abiraterone 1000 mg PO QD
Phase II: Arm 1EXPERIMENTALTulmimetostat dose 1 PO + Darolutamide 600 mg PO BID
Phase II: Arm 2EXPERIMENTALTulmimetostat dose 2 PO + Darolutamide 600 mg PO BID
Phase II: Arm 3ACTIVE_COMPARATORDarolutamide 600 mg PO BID
Dose De-Escalation Cohort: Tulmimetostat (DZR123)EXPERIMENTALDaily DZR123 by mouth for days 1-28 of each 28-day cycle. Dose will depend on dose level assignment of 300 mg daily, 250 mg daily, or 200 mg daily.
Dose Expansion Cohort: Tulmimetostat (DZR123) - 300 mgEXPERIMENTALDaily DZR123by mouth for days 1-28 of each 28-day cycle. Dose will be the maximum-tolerated dose found during the dose de-escalation cohort which was 300 mg.
Dose Expansion Cohort: Tulmimetostat (DZR123) - 200 mgEXPERIMENTALDaily DZR123 by mouth for days 1-28 of each 28-day cycle. Dose will be 200 mg as the maximum tolerated dose of 300 mg found during the initial dose expansion cohort caused numerous dose reductions.
Phase 1EXPERIMENTALEligible participants with advanced tumors will receive escalating doses of Tulmimetostat once per day orally.
Phase 2 - Cohort M1 (Advanced/metastatic solid tumors or urothelial carcinoma with ARID1A mutation)EXPERIMENTALEligible participants with advanced/metastatic solid tumors (excluding ovarian clear cell and endometrial carcinoma) or urothelial carcinoma, confirmed to have ARID1A mutations will receive oral Tulmimetostat once daily in 28-day treatment cycles.
Phase 2 - Cohort M2 (Ovarian clear cell carcinoma with ARID1A mutation)EXPERIMENTALEligible participants with advanced ovarian clear cell carcinoma, confirmed to have ARID1A mutations, who have received prior platinum-based chemotherapy will receive oral Tulmimetostat once daily in 28-day treatment cycles.
Phase 2 - Cohort M3 (Endometrial carcinoma with ARID1A mutation)EXPERIMENTALEligible participants with recurrent, metastatic, or unresectable endometrial carcinoma, confirmed to have ARID1A mutations, and prior platinum-based therapy will receive oral Tulmimetostat once daily in 28-day treatment cycles.
Phase 2 - Cohort M4 (Relapsed/refractory lymphoma (PTCL or DLBCL))EXPERIMENTALEligible participants with relapsed or refractory peripheral T-cell lymphoma (PTCL) or diffuse large B-cell lymphoma (DLBCL), including those with EZH2 hotspot mutations will receive oral Tulmimetostat once daily in 28-day treatment cycles.
Phase 2 - Cohort M5 (Malignant mesothelioma with BAP1 loss)EXPERIMENTALEligible participants with relapsed or refractory malignant pleural or peritoneal mesothelioma, confirmed to have BAP1 loss will receive oral Tulmimetostat once daily in 28-day treatment cycles.
Phase 2 - Cohort M6 (Metastatic castration-resistant prostate cancer (mCRPC))EXPERIMENTALEligible participants with mCRPC, measurable soft tissue disease, and prior treatment with at least one androgen receptor signaling inhibitor and one taxane-based chemotherapy will receive oral Tulmimetostat once daily in 28-day treatment cycles.
Phase 2 - Cohort M7 (Food effect in ARID1A wildtype endometrial carcinoma)EXPERIMENTALEligible participants with recurrent, advanced endometrial carcinoma that is ARID1A wildtype (no ARID1A mutation), to evaluate the effect of food on DZR123 pharmacokinetics will receive oral Tulmimetostat once daily in 28-day treatment cycles.
Cohort M8 - Part 1 (Tulmimetostat + enzalutamide in mCRPC)EXPERIMENTALEligible participants with mCRPC receive DZR123 in combination with enzalutamide. Part 1 is dose escalation to determine the recommended dose.
Cohort M8 - Part 2 (Tulmimetostat + enzalutamide in mCRPC)EXPERIMENTALEligible participants with mCRPC receive DZR123 in combination with enzalutamide. Part 2 is expansion at the selected dose to further assess safety and antitumor activity.

Interventions

NameTypeDescription
TulmimetostatDRUGDoses of tulmimetostat beyond DL1 once a day (QD) will be opened depending on outcome of Dose Escalation Meetings (DEM(s))
DarolutamideDRUG600 mg is administered orally BID
AbirateroneDRUG1000 mg is administered orally QD
EnzalutamideDRUGEnzalutamide dosed once per day orally in 28 day cycles
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Eligibility Criteria

Age Range18 Years to N/A
SexMALE
Healthy VolunteersNo
Study Sites31

Key Inclusion Criteria: * Adult men ≥ 18 years old with de novo or recurrent mHSPC (without neuroendocrine or small cell features). The tumor lesion(s) may be located in the bone, soft tissue/visceral region, or both. * Participants must have castrate levels of testosterone, i.e., ≤ 50 ng/dL (≤ 1.7...

Countries:United StatesAustraliaBrazilCanadaChinaFranceGermanyHong KongHungaryItalySouth KoreaSpainTurkey (Türkiye)United KingdomPoland
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Competitive Landscape -Other Solid Tumors 9 trials (matched to "Advanced Solid Tumor")

Recent Changes (Last 90 Days)

LOWAug 20, 2026NCT04104776lastUpdatePostDate: changed
LOWAug 20, 2026NCT04104776lastUpdatePostDate: changed
LOWAug 20, 2026NCT04104776lastUpdatePostDate: changed
LOWAug 20, 2026NCT04104776lastUpdatePostDate: changed
LOWJul 17, 2026NCT04104776Enrollment: 275 → 300
LOWJul 17, 2026NCT04104776Enrollment: 275 → 300
LOWJun 23, 2026NCT07190300lastUpdatePostDate: changed
LOWJun 23, 2026NCT07190300lastUpdatePostDate: changed
LOWJun 22, 2026NCT04104776lastUpdatePostDate: changed
LOWJun 22, 2026NCT04104776lastUpdatePostDate: changed
LOWJun 9, 2026NCT07190300lastUpdatePostDate: changed
LOWJun 9, 2026NCT07190300lastUpdatePostDate: changed
LOWJun 9, 2026NCT07190300lastUpdatePostDate: changed
LOWJun 9, 2026NCT07190300lastUpdatePostDate: changed

Frequently asked questions about Tulmimetostat

What is Tulmimetostat used for?

Tulmimetostat is an investigational small molecule being studied in oncology for advanced solid tumors, mycosis fungoides, and metastatic hormone-sensitive prostate cancer (mHSPC). It is also being evaluated in lymphomas and other cancer types. The drug is in Phase 1 clinical development.

What does Tulmimetostat target?

Tulmimetostat is an enzyme inhibitor, belonging to the -stat class of drugs. It is being studied for its effects on cancer cell growth in solid tumors and lymphomas. The specific molecular target is not disclosed in the available information.

Who is developing Tulmimetostat?

Tulmimetostat is being developed by Novartis AG, a global pharmaceutical company listed on the New York Stock Exchange under the ticker NVS. The drug is currently in Phase 1 clinical trials for multiple oncology indications.

What phase is Tulmimetostat in?

Tulmimetostat is in Phase 1 clinical development. It is an investigational drug and has not been approved by regulatory authorities. Multiple Phase 1 trials are ongoing or have been completed to evaluate its safety and efficacy in various cancers.

What clinical trials is Tulmimetostat in?

Tulmimetostat is being studied in several clinical trials. NCT04104776 is a Phase 1 study in advanced solid tumors and lymphomas. NCT05944562 is a Phase 1 trial in mycosis fungoides and Sézary syndrome. NCT07190300 is a Phase 1/II study in metastatic hormone-sensitive prostate cancer.

Is Tulmimetostat the same as CPI-0209?

Yes, Tulmimetostat is also known as DZR123 and CPI-0209. These names refer to the same investigational drug being developed by Novartis. In clinical trial records, the drug is sometimes listed under these alternative identifiers.