Recent Updates
Recently added Catalysts

AVI-4658

Phase 1

Duchenne Muscular Dystrophy | Small molecule | Neurology |United Therapeutics Corporation|Last Updated: Dec 5, 2019

Success Probability
Approval Probability 71%
TA Base Rate26%
Adjusted LOA41%
ML RiskLOW_RISK
Premium
Market & Valuation
rNPV $3.2B
Market Size $9.4B
Revenue Basis $1.6B
Competitors 6
Premium
Trial Design
CONTROLLEDDMCBiomarker
Total Trials1
Total Enrollment7
FDA Designations
No designations recorded
Clinical Trials (1)
NCT IDTitlePhaseStatusEnrollmentVelocityDesignStartCompletionLast UpdatedSitesCountries
NCT00159250Safety and Efficacy Study of Antisense Oligonucleotides in Duchenne Muscular DystrophyPHASE1 COMPLETED 7Oct 26, 2007Mar 31, 2009Dec 5, 20191 United Kingdom
Unlock Drug Trial Details
Study Endpoints
Primary Endpoints
Number of Participants With Adverse Events Related to AVI-4568
Baseline up to Day 120

Number of Subjects with Treatment Emergent Adverse Events (TEAEs) and Serious TEAEs

Number of Participants With Injection Site Reactions
From the Day of Screening to Day 3
Number of Subjects With Clinically Significant Change From Baseline in Laboratory Values
From the Day of Screening up to Day 28

Assessed by light microscopy and immunocytochemistry to detect the differences in inflammatory infiltrates between the AVI-4568 and placebo-treated EDB muscles

Secondary Endpoints
Number of Participants With Induced Skipping of Exon 51 in the Treated Extensor Digitorum Brevis (EDB) Muscle Determined by Reverse Transcription Polymerase Chain Reaction
Day 14 to Day 28
Number of Participants With Restoration of Dystrophin Protein Expression Measured by Immunocytochemistry
Day 14 to Day 28
Number of Participants With Restoration of Dystrophin Protein Expression Measured by Western Blot Analysis
Day 14 to Day 28
Unlock Study Endpoints
Study Design & Arms
AllocationNON_RANDOMIZED
MaskingSINGLE
ModelSINGLE_GROUP
PurposeTREATMENT
Treatment Arms
ArmTypeDescription
Low doseEXPERIMENTALLow dose of AVI-4658
High doseEXPERIMENTALHigh dose of AVI-4658
Interventions
NameTypeDescription
AVI-4658 (PMO)DRUGmorpholino antisense oligonucleotide
Unlock Study Design Details
Eligibility Criteria
Age Range10 Years — 17 Years
SexMALE
Healthy VolunteersNo
Study Sites1

Inclusion Criteria: 1. Subject is male ≥ 10 years and ≤ 17 years of age at the time of study drug administration. 2. Subject has clinical diagnosis compatible with Duchenne's Muscular Dystrophy (DMD) and evidence of mutational and dystrophin defects from muscle biopsy consistent with DMD (out-of fr...

Countries:United Kingdom
Unlock Eligibility Criteria