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gene therapy

Phase 1

Aromatic L-amino Acid Decarboxylase (AADC) Deficiency | Small molecule | Other |PTC Therapeutics, Inc.|Last Updated: Feb 10, 2023

Success Probability
Approval Probability 71%
TA Base Rate26%
Adjusted LOA41%
ML RiskLOW_RISK
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Market & Valuation
rNPV $3.2B
Market Size $9.4B
Revenue Basis $1.6B
Competitors 6
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Trial Design
UNCONTROLLEDDMCBiomarker
Total Trials1
Total Enrollment10
FDA Designations
No designations recorded
Clinical Trials (1)
NCT IDTitlePhaseStatusEnrollmentVelocityDesignStartCompletionLast UpdatedSitesCountries
NCT01395641A Phase I/II Clinical Trial for Treatment of Aromatic L-amino Acid Decarboxylase (AADC) Deficiency Using AAV2-hAADCPHASE1 COMPLETED 10Oct 22, 2014Mar 7, 2022Feb 10, 20231 Taiwan
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Study Endpoints
Primary Endpoints
Evaluation of therapeutic effect
12 months

1. At one year post-surgery, neurotransmitter metabolites (HVA or HIAA) is detectable in CSF (higher than that at pre-surgery) 2. At one year post-surgery, PDMS-II score is higher than that at pre-surgery, with an improvement over 10 points

Secondary Endpoints
Evaluation of safety and other therapeutic effects Evaluation for the treatment safety
12 months
Evaluation of secondary therapeutic effects
5 years
Exploratory endpoint
5 years
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Study Design & Arms
AllocationNA
MaskingNONE
ModelSINGLE_GROUP
PurposeTREATMENT
Treatment Arms
ArmTypeDescription
Gene therapyEXPERIMENTALIntracerebral infusion of AAV2-hAADC viral vector will be performed
Interventions
NameTypeDescription
gene therapyDRUGAAV2-hAADC viral vector will be injected into bilateral putamen by stereotactic surgery.
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Eligibility Criteria
Age Range24 Months — N/A
SexALL
Healthy VolunteersNo
Study Sites1

Inclusion Criteria: 1. With a confirmed diagnosis of AADC, including cerebrospinal fluid analysis to show reduced levels of neurotransmitter metabolites, HVA and 5-HIAA, and higher L-Dopa, together with more than one mutation within AADC gene. 2. Classical clinical characteristics of AADC deficienc...

Countries:Taiwan
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