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BMN 110 - Weekly

Phase 3

Mucopolysaccharidosis IV A | Small molecule | Rare Disease |BioMarin Pharmaceutical Inc.|Last Updated: Jul 21, 2021

Success Probability
Approval Probability 71%
TA Base Rate26%
Adjusted LOA41%
ML RiskLOW_RISK
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Market & Valuation
rNPV $3.2B
Market Size $9.4B
Revenue Basis $1.6B
Competitors 6
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Trial Design
RandomizedDouble-BlindCONTROLLEDDMCBiomarker
Total Trials1
Total Enrollment173
FDA Designations
No designations recorded
Clinical Trials (1)
NCT IDTitlePhaseStatusEnrollmentVelocityDesignStartCompletionLast UpdatedSitesCountries
NCT01415427Long-Term Efficacy and Safety Extension Study of BMN 110 in Patients With Mucopolysaccharidosis IVA (Morquio A Syndrome)PHASE3 COMPLETED 173Jul 1, 2011Jun 16, 2016Jul 21, 202143 United States, Argentina +18
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Study Endpoints
Primary Endpoints
Change From Baseline in 6-minute Walk (6MW) Test - ITT
Baseline to week 168

Efficacy was assessed by changes from baseline in 6-minute walk test

Change From Baseline in 6-minute Walk (6MW) Test - MPP
Baseline to week 168

Efficacy was assessed by changes from baseline in 6-minute walk test

Secondary Endpoints
Change From Baseline in 3-minute Stair Climb Test - ITT
Baseline to week 168
Change From Baseline in 3-minute Stair Climb Test - MPP
Baseline to week 168
Change From Baseline in Urine Keratan Sulfate - ITT
Baseline to week 168
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Study Design & Arms
AllocationRANDOMIZED
MaskingQUADRUPLE
ModelPARALLEL
PurposeTREATMENT
Treatment Arms
ArmTypeDescription
BMN 110 WeeklyEXPERIMENTALBMN 110 Weekly: In Part 1, patients will receive an intravenous infusion of BMN 110 at a dose of 2.0 mg/kg administered over a period of approximately 4 hours once a week.
BMN 110 Every Other WeekEXPERIMENTALBMN 110 Every Other Week: In Part 1, patients will receive an intravenous infusion of BMN 110 at a dose of 2.0 mg/kg administered over a period of approximately 4 hours every other week and will receive infusions of placebo on alternating weeks.
Interventions
NameTypeDescription
BMN 110 - WeeklyDRUGIn Part 1, patients will receive intravenous (IV) infusions of study drug at a dose of 2.0 mg/kg/qw administered over a period of approximately 4 hours once a week. In Part 2, patients will continue to receive 2.0 mg/kg of BMN 110 every week, with no placebo.
BMN 110 - Every Other WeekDRUGIn Part 1, patients will receive intravenous (IV) infusions of study drug at a dose of 2.0 mg/kg administered over a period of approximately 4 hours every other week. Patients randomized to the 2.0 mg/kg/qow arm will receive infusions of placebo on alternating weeks, to mask active drug weeks. In Part 2, patients will receive 2.0 mg/kg of BMN 110 every week, with no placebo.
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Eligibility Criteria
Age Range5 Years — N/A
SexALL
Healthy VolunteersNo
Study Sites43

Inclusion Criteria: * Must have completed MOR-004 * Is willing and able to provide written, signed informed consent. Or in the case of patients under the age of 18 (or other age as defined by regional law or regulation), provide written assent (if required) and have written informed consent, signed...

Countries:United StatesArgentinaBrazilCanadaColombiaDenmarkFranceGermanyItalyJapanNetherlandsNorwayPortugalQatarSaudi ArabiaSouth KoreaSpainTaiwanTurkey (Türkiye)United Kingdom
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